The compartmentalisation of phosphorylated free oligosaccharides in cells from a CDG Ig patient reveals a novel ER-to-cytosol translocation process

PLoS ONE

Volumn 5, Issue 7, 2010, Pages

  Peric, Delphine ^a,b,i   Durrant Arico, Christelle ^a,b,j   Delenda, Christophe ^c,k   Dupré, Thierry ^a,b,d   de Lonlay, Pascale ^e   de Baulny, Hélène Ogier ^f   Pelatan, Cécile ^g   Bader Meunier, Brigitte ^h   Danos, Olivier ^c,e   Chantret, Isabelle ^a,b   Moore, Stuart E H ^a,b  

^a CENTRE DE RECHERCHE BIOMÉDICALE BICHAT BEAUJON CRB3   (France)

^b UNIVERSITÉ PARIS DESCARTES   (France)

^c GÉNÉTHON   (France)

^d BICHAT HOSPITAL   (France)

^e HÔPITAL NECKER ENFANTS MALADES   (France)

^f HÔPITAL ROBERT DEBRÉ   (France)

^g CENTRE HOSPITALIER   (France)

^h BICÊTRE HOSPITAL   (France)

ⁱ INSTITUT DE RADIOBIOLOGIE CELLULAIRE ET MOLÉCULAIRE   (France)

^j GLYCODE SAS   (France)

^k Arvid Wallgrens Backe 20   (France)

more..

Author keywords

[No Author keywords available]

Indexed keywords

DOLICHOL; HEXOSE; INORGANIC PYROPHOSPHATASE; OLIGOSACCHARIDE;

ARTICLE; CELL COMPARTMENTALIZATION; CELL COUNT; CELL MEMBRANE PERMEABILITY; CELL TRANSFORMATION; CELL TRANSPORT; CELL VACUOLE; CONGENITAL DISORDER OF GLYCOSYLATION TYPE 1G; CONTROLLED STUDY; CYTOSOL; ENDOPLASMIC RETICULUM; EPSTEIN BARR VIRUS; GLYCOSYLATION; HUMAN; HUMAN CELL; ISOTOPE LABELING; LYMPHOBLASTOID CELL; PHOSPHORYLATION; PROTEIN SYNTHESIS; ANIMAL; BIOLOGICAL MODEL; CELL LINE; DISORDERS OF CARBOHYDRATE METABOLISM; LYMPHOMA; METABOLISM; MOUSE; PHYSIOLOGY; TUMOR CELL LINE;

HUMAN HERPESVIRUS 4;

ANIMALS; CARBOHYDRATE METABOLISM, INBORN ERRORS; CELL LINE; CELL LINE, TUMOR; GLYCOSYLATION; HUMANS; LYMPHOMA; MICE; MODELS, BIOLOGICAL; OLIGOSACCHARIDES; PHOSPHORYLATION;

EID: 77955353172     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0011675     Document Type: Article

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