Misfolded endoplasmic reticulum retained subunits cause degradation of wild-type subunits of arylsulfatase A heteromers

FEBS Journal

Volumn 277, Issue 16, 2010, Pages 3404-3414

  Poeppel, Peter ^a   Abouzied, Mekky Mohamed ^a,b   Völker, Christof ^a   Gieselmann, Volkmar ^a  

^a UNIVERSITY OF BONN   (Germany)

^b Minia University   (Egypt)

Author keywords

arylsulfatase A; ERAD; MLD; protein oligomerization; protein quality control

Indexed keywords

CEREBROSIDE SULFATASE; PROTEIN SUBUNIT;

ANIMAL CELL; ARTICLE; ENDOPLASMIC RETICULUM; ENZYME ANALYSIS; ENZYME SUBUNIT; NONHUMAN; PRIORITY JOURNAL; PROTEIN CONFORMATION; PROTEIN FOLDING; QUALITY CONTROL; WILD TYPE;

ANIMALS; BLOTTING, WESTERN; CELL LINE; CELLS, CULTURED; CEREBROSIDE-SULFATASE; CRICETINAE; DIMERIZATION; ENDOPLASMIC RETICULUM; LYSOSOMES; MODELS, BIOLOGICAL; MUTATION; PROTEIN FOLDING;

EID: 77955236789     PISSN: 1742464X     EISSN: 17424658     Source Type: Journal    
DOI: 10.1111/j.1742-4658.2010.07745.x     Document Type: Article

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