Effect of pharmacological chaperones on brain tyrosine hydroxylase and tryptophan hydroxylase 2

Journal of Neurochemistry

Volumn 114, Issue 3, 2010, Pages 853-863

  Calvo, Ana C ^a   Scherer, Tanja ^b   Pey, Angel L ^a,c   Ying, Ming ^a   Winge, Ingeborg ^a   McKinney, Jeffrey ^a   Haavik, Jan ^a   Thöny, Beat ^b   Martinez, Aurora ^a  

^a UNIVERSITY OF BERGEN   (Norway)

^b UNIVERSITY OF ZURICH   (Switzerland)

^c UNIVERSITY OF GRANADA   (Spain)

Author keywords

l DOPA responsive dystonia; pharmacological chaperones; tryptophan hydroxylase; tyrosine hydroxylase

Indexed keywords

1 BENZHYDRYL 4 (1 METHYL 4 NITRO 1H IMIDAZOL 5 YL)PIPERAZINE; 3 AMINO 2 BENZYL 7 NITRO 4 (2 QUINOLYL) 1,2 DIHYDROISOQUINOLIN 1 ONE; 3,4 DIHYDROXYPHENYLACETIC ACID; 5 AMINO 3 (5 METHYL 3 PHENYL 4 ISOXAZOLYL) 1H PYRAZOLE 4 CARBONITRILE; 5 HYDROXYINDOLEACETIC ACID; 5,6 DIMETHYL 3 (4 METHYL 2 PYRIDINYL) 2 THIOXO 2,3 DIHYDROTHIENO[2,3 D]PYRIMIDIN 4(1H) ONE; CHAPERONE; DOPAMINE; HOMOVANILLIC ACID; LEVODOPA; SEROTONIN; TETRAHYDROBIOPTERIN; TRYPTOPHAN HYDROXYLASE 2; TYROSINE 3 MONOOXYGENASE; UNCLASSIFIED DRUG; BIOGENIC AMINE; PHENYLALANINE 4 MONOOXYGENASE; TPH2 PROTEIN, MOUSE; TRYPTOPHAN HYDROXYLASE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CIRCULAR DICHROISM; CONTROLLED STUDY; DYSTONIA; ENZYME ACTIVITY; ENZYME DENATURATION; ENZYME KINETICS; FLUOROMETRY; GENE EXPRESSION; IMMUNODETECTION; MOUSE; NONHUMAN; PHENYLKETONURIA; PRIORITY JOURNAL; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; WILD TYPE; ANIMAL; BIOSYNTHESIS; BRAIN; C57BL MOUSE; CHEMISTRY; DRUG EFFECTS; DYSTONIC DISORDERS; ENZYME STABILITY; ENZYMOLOGY; GENETICS; HUMAN; METABOLISM; MUTATION; PROTEIN FOLDING;

MUS;

ANIMALS; BIOGENIC MONOAMINES; BRAIN; DYSTONIC DISORDERS; ENZYME STABILITY; HUMANS; MICE; MICE, INBRED C57BL; MOLECULAR CHAPERONES; MUTATION; PHENYLALANINE HYDROXYLASE; PROTEIN FOLDING; TRYPTOPHAN HYDROXYLASE; TYROSINE 3-MONOOXYGENASE;

EID: 77954336730     PISSN: 00223042     EISSN: 14714159     Source Type: Journal    
DOI: 10.1111/j.1471-4159.2010.06821.x     Document Type: Article

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