Making the most of what you've got: Optimizing residual OXPHOS function in mitochondrial diseases

EMBO Molecular Medicine

Volumn 1, Issue 8-9, 2009, Pages 357-359

  Moraes, Carlos T ^a  

^a UNIVERSITY OF MIAMI MILLER SCHOOL OF MEDICINE   (United States)

Author keywords

Cytochrome oxydase; Mitochondrial diseases; Oxphos; PGC 1alpha; Ros

Indexed keywords

ADENOSINE TRIPHOSPHATE; ADENYLATE CYCLASE; ANTIOXIDANT; CYCLIC AMP DEPENDENT PROTEIN KINASE; CYCLIC AMP DEPENDENT PROTEIN KINASE AGONIST; CYCLIC AMP DEPENDENT PROTEIN KINASE INHIBITOR; CYTOCHROME C OXIDASE; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA COACTIVATOR 1ALPHA; REACTIVE OXYGEN METABOLITE; UNCLASSIFIED DRUG;

BIOGENESIS; BRAIN DISEASE; CAENORHABDITIS ELEGANS; CELL PROLIFERATION; CYTOCHROME C OXIDASE DEFICIENCY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVATION; ENZYME ACTIVITY; ENZYME REGULATION; ENZYME SUBSTRATE; FAMILIAL INCIDENCE; GENE MUTATION; HUMAN; MITOCHONDRIAL RESPIRATION; MYOPATHY; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; SHORT SURVEY; SIGNAL TRANSDUCTION; UPREGULATION;

ADENOSINE TRIPHOSPHATE; CYCLIC AMP-DEPENDENT PROTEIN KINASES; ELECTRON TRANSPORT COMPLEX IV; HUMANS; MITOCHONDRIA; MITOCHONDRIAL DISEASES; OXIDATIVE PHOSPHORYLATION;

EID: 77953668597     PISSN: 17574676     EISSN: 17574684     Source Type: Journal    
DOI: 10.1002/emmm.200900049     Document Type: Short Survey

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