Congenital long QT syndrome and 2:1 atrioventricular block: An optimistic outcome in the current era

Heart Rhythm

Volumn 7, Issue 6, 2010, Pages 781-785

  Aziz, Peter F ^a   Tanel, Ronn E ^b   Zelster, Ilana J ^c   Pass, Robert H ^d   Wieand, Tammy S ^a   Vetter, Victoria L ^a   Vogel, R Lee ^a   Shah, Maully J ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c CHILDREN S MEDICAL CENTER   (United States)

^d ALBERT EINSTEIN COLLEGE OF MEDICINE   (United States)

Author keywords

Atrioventricular block; Long QT syndrome; Torsades de pointes

Indexed keywords

ATENOLOL; BETA ADRENERGIC RECEPTOR BLOCKING AGENT; ESMOLOL; FLECAINIDE; MEXILETINE; NADOLOL; POTASSIUM CHANNEL; POTASSIUM CHANNEL KCNH2; PROPRANOLOL; SODIUM CHANNEL NAV1.5; UNCLASSIFIED DRUG;

2:1 ATRIOVENTRICULAR BLOCK; ADOLESCENT; ARTICLE; ATRIOVENTRICULAR BLOCK; AUTONOMIC DENERVATION; BRADYCARDIA; CHILD; DEFIBRILLATOR; DEVICE THERAPY; ELECTROCARDIOGRAM; FAMILY HISTORY; FEMALE; GENE MUTATION; GENOTYPE; HEART ARREST; HEART DENERVATION; HIGH RISK POPULATION; HUMAN; LONG QT SYNDROME; MAJOR CLINICAL STUDY; MALE; MORTALITY; PACEMAKER; PRIMARY PREVENTION; PRIORITY JOURNAL; QT INTERVAL; RESUSCITATION; RETROSPECTIVE STUDY; SECONDARY PREVENTION; SUDDEN DEATH; SYMPATHETIC NERVE; SYNCOPE; TORSADE DES POINTES; TREATMENT INDICATION;

ADRENERGIC BETA-ANTAGONISTS; ANTI-ARRHYTHMIA AGENTS; ATRIOVENTRICULAR BLOCK; CHILD; CHILD, PRESCHOOL; COHORT STUDIES; DEFIBRILLATORS, IMPLANTABLE; FEMALE; FLECAINIDE; GENOTYPE; HUMANS; INFANT; INFANT, NEWBORN; LONG QT SYNDROME; MALE; MEXILETINE; MULTIVARIATE ANALYSIS; PROGNOSIS; PROPANOLAMINES; PROPRANOLOL; RETROSPECTIVE STUDIES; RISK ASSESSMENT; RISK FACTORS; TORSADES DE POINTES; TREATMENT OUTCOME;

EID: 77952539116     PISSN: 15475271     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.hrthm.2010.02.035     Document Type: Article

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