Long QT syndrome due to a novel mutation in SCN5A: Treatment with ICD placement at 1 month and left cardiac sympathetic denervation at 3 months of age

Journal of Interventional Cardiac Electrophysiology

Volumn 26, Issue 1, 2009, Pages 41-45

  Silver, Eric S ^a   Liberman, Leonardo ^a   Chung, Wendy K ^a   Spotnitz, Henry M ^a   Chen, Jonathan M ^a   Ackerman, Michael J ^b   Moir, Christopher ^b   Hordof, Allan J ^a   Pass, Robert H ^c  

^a Och Spine at New York Presbyterian Hospitals   (United States)

^b MAYO CLINIC   (United States)

^c ALBERT EINSTEIN COLLEGE OF MEDICINE   (United States)

Author keywords

Implantable cardioverter defibrillator; Long QT Syndrome; Pediatric; SCN5A; Sympathectomy

Indexed keywords

ADRENALIN; CALCIUM; ESMOLOL; FLECAINIDE; ISOPRENALINE; LIDOCAINE; MAGNESIUM; MEXILETINE; PROPRANOLOL;

ARTICLE; CASE REPORT; DEFIBRILLATION; DEFIBRILLATOR; DRUG DOSE INCREASE; DRUG DOSE TITRATION; ELECTROCARDIOGRAPHY; GENE; GENE MUTATION; HUMAN; LONG QT SYNDROME; MALE; NEWBORN; NEWBORN CARE; PHYSICAL EXAMINATION; PRIORITY JOURNAL; SCN5A GENE; TORSADE DES POINTES;

COMBINED MODALITY THERAPY; DEFIBRILLATORS, IMPLANTABLE; HUMANS; INFANT, NEWBORN; LONG QT SYNDROME; MALE; MUSCLE PROTEINS; MUTATION; POLYMORPHISM, SINGLE NUCLEOTIDE; SODIUM CHANNELS; SYMPATHECTOMY; TREATMENT OUTCOME;

EID: 70349332479     PISSN: 1383875X     EISSN: 15728595     Source Type: Journal    
DOI: 10.1007/s10840-009-9428-1     Document Type: Article

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