Mechanisms underlying metabolic and neural defects in zebrafish and human multiple Acyl-CoA dehydrogenase deficiency (MADD)

PLoS ONE

Volumn 4, Issue 12, 2009, Pages

  Song, Yuanquan ^a   Selak, Mary A ^b   Watson, Corey T ^c   Coutts, Christopher ^d   Scherer, Paul C ^a   Panzer, Jessica A ^a   Gibbs, Sarah ^a   Scott, Marion O ^a   Willer, Gregory ^c   Gregg, Ronald G ^c   Ali, Declan W ^d   Bennett, Michael J ^a   Balice Gordon, Rita J ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

^c UNIVERSITY OF LOUISVILLE   (United States)

^d UNIVERSITY OF ALBERTA   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

ACYL COENZYME A DEHYDROGENASE; ELECTRON TRANSFERRING FLAVOPROTEIN; MITOGEN ACTIVATED PROTEIN KINASE; MUTANT PROTEIN; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA AGONIST; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA ANTAGONIST;

AEROBIC METABOLISM; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL PROLIFERATION; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; EMBRYO; FIBROBLAST; GLYCOLYSIS; HUMAN; HUMAN CELL; METABOLIC DISORDER; MULTIPLE ACYL COA DEHYDROGENASE DEFICIENCY; NERVOUS SYSTEM DEVELOPMENT; NEUROLOGIC DISEASE; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PARALYSIS; PHENOTYPE; SIGNAL TRANSDUCTION; UPREGULATION; WILD TYPE; ZEBRA FISH;

ANIMALS; CARBOXYLIC ACIDS; CARNITINE; CELL PROLIFERATION; CLONING, MOLECULAR; ELECTRON-TRANSFERRING FLAVOPROTEINS; ENZYME ACTIVATION; EXTRACELLULAR SIGNAL-REGULATED MAP KINASES; FIBROBLASTS; GLYCOLYSIS; HUMANS; INFANT; INFANT, NEWBORN; IRON-SULFUR PROTEINS; MITOCHONDRIA; MULTIPLE ACYL COENZYME A DEHYDROGENASE DEFICIENCY; MUTATION; NERVOUS SYSTEM; NEURONS; OLIGONUCLEOTIDES, ANTISENSE; OXIDOREDUCTASES ACTING ON CH-NH GROUP DONORS; PEROXISOME PROLIFERATOR-ACTIVATED RECEPTORS; PHENOTYPE; ZEBRAFISH;

DANIO RERIO;

EID: 77949535658     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0008329     Document Type: Article

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