Conventional diet therapy for hyperammonemia is risky in the treatment of hepatic encephalopathy associated with citrin deficiency

Internal Medicine

Volumn 49, Issue 3, 2010, Pages 243-247

  Fukushima, Kazuhiro ^a   Yazaki, Masahide ^a   Nakamura, Mio ^a   Tanaka, Naoki ^a   Kobayashi, Keiko ^b   Saheki, Takeyori ^c   Takei, Hideki ^d   Ikeda, Shu Ichi ^a  

^a SHINSHU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b KAGOSHIMA UNIVERSITY   (Japan)

^c TOKUSHIMA BUNRI UNIVERSITY   (Japan)

^d Suwa Red Cross Hospital   (Japan)

Author keywords

Carbohydrate; Citrin deficiency; CTLN2; Low protein diet

Indexed keywords

ALANINE AMINOTRANSFERASE; AMMONIA; APROTININ; ARGININE; ASPARTATE AMINOTRANSFERASE; BRANCHED CHAIN AMINO ACID; CARBOHYDRATE; CITRULLINE; GAMMA GLUTAMYLTRANSFERASE; KANAMYCIN; LACTULOSE;

ADULT; ALANINE AMINOTRANSFERASE BLOOD LEVEL; AMMONIA BLOOD LEVEL; ARTICLE; ASPARTATE AMINOTRANSFERASE BLOOD LEVEL; AUTOSOMAL RECESSIVE DISORDER; CALORIC INTAKE; CARBOHYDRATE ANALYSIS; CASE REPORT; CHRONIC DISEASE; CITRIN DEFICIENCY; CITRULLINEMIA; CITRULLINEMIA TYPE II; CONFUSION; CONSCIOUSNESS DISORDER; DIET THERAPY; DISEASE ASSOCIATION; DISEASE COURSE; DNA DETERMINATION; ELECTROENCEPHALOGRAM; FAT CONTENT; FATTY LIVER; FISH; FLAPPING TREMOR; FOOD PREFERENCE; GAMMA GLUTAMYL TRANSFERASE BLOOD LEVEL; GENE MUTATION; GENERAL CONDITION DETERIORATION; HAND; HEPATIC ENCEPHALOPATHY; HETEROZYGOTE; HUMAN; HYPERAMMONEMIA; IRRITABILITY; LIVER BIOPSY; LIVER FAILURE; LOW CARBOHYDRATE DIET; MALE; MILK; NEUROLOGIC EXAMINATION; PEANUT; PROTEIN BLOOD LEVEL; PROTEIN CONTENT; PROTEIN RESTRICTION; RISK ASSESSMENT;

ARGININE; CITRULLINEMIA; DIET, PROTEIN-RESTRICTED; DIETARY SUPPLEMENTS; GENE DELETION; HEPATIC ENCEPHALOPATHY; HUMANS; HYPERAMMONEMIA; MALE; MIDDLE AGED; MITOCHONDRIAL MEMBRANE TRANSPORT PROTEINS;

EID: 77749260578     PISSN: 09182918     EISSN: 13497235     Source Type: Journal    
DOI: 10.2169/internalmedicine.49.2712     Document Type: Article

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