Deafness and retinal degeneration in a novel USH1C knock-in mouse model

Developmental Neurobiology

Volumn 70, Issue 4, 2010, Pages 253-267

  Lentz, Jennifer J ^a,b   Gordon, William C ^a,b   Farris, Hamilton E ^b   MacDonald, Glen H ^c   Cunningham, Dale E ^c   Robbins, Carol A ^c   Tempel, Bruce L ^c   Bazan, Nicolas G ^a,b   Rubel, Edwin W ^c   Oesterle, Elizabeth C ^c   Keats, Bronya J ^a,d  

^a LOUISIANA STATE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b LOUISIANA STATE UNIVERSITY HEALTH SCIENCES CENTER   (United States)

^c UNIVERSITY OF WASHINGTON   (United States)

^d AUSTRALIAN NATIONAL UNIVERSITY   (Australia)

Author keywords

Deafness; Mouse model; Retinal degeneration; Usher syndrome

Indexed keywords

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; ELECTRORETINOGRAM; EVOKED AUDITORY RESPONSE; EVOKED BRAIN STEM RESPONSE; HAIR CELL; HEARING IMPAIRMENT; HISTOLOGY; IMMUNOFLUORESCENCE; MOUSE; NONHUMAN; PHOTORECEPTOR; PRIORITY JOURNAL; RETINA DEGENERATION; SCANNING ELECTRON MICROSCOPY;

ADAPTOR PROTEINS, SIGNAL TRANSDUCING; AGING; ANIMALS; COCHLEA; DEAFNESS; DISEASE MODELS, ANIMAL; ELECTRORETINOGRAPHY; EVOKED POTENTIALS, AUDITORY, BRAIN STEM; EXONS; GENE KNOCK-IN TECHNIQUES; HAIR CELLS, AUDITORY; LOUISIANA; MICE; MICE, TRANSGENIC; MUTATION, MISSENSE; RETINA; RETINAL DEGENERATION; RETINAL ROD PHOTORECEPTOR CELLS; RNA SPLICE SITES; RNA, MESSENGER; USHER SYNDROMES;

EID: 77649114893     PISSN: 19328451     EISSN: 10974695     Source Type: Journal    
DOI: 10.1002/dneu.20771     Document Type: Article

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