Cone versus rod disease in a mutant RPGR mouse caused by different genetic backgrounds

Investigative Ophthalmology and Visual Science

Volumn 51, Issue 2, 2010, Pages 1106-1115

  Brunner, Sandra ^a   Skosyrski, Sergej ^b   Kirschner Schwabe, Renate ^b   Knobeloch, Klaus Peter ^c,d   Neidhardt, John ^a   Feil, Silke ^a   Glaus, Esther ^a   Luhmann, Ulrich F O ^e   Rüther, Klaus ^b   Berger, Wolfgang ^a  

^a UNIVERSITY OF ZURICH   (Switzerland)

^b CHARITÉ UNIVERSITÄTSMEDIZIN BERLIN   (Germany)

^c LEIBNIZ INSTITUT FÜR MOLEKULARE PHARMAKOLOGIE   (Germany)

^d UNIVERSITY OF FREIBURG   (Germany)

^e UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

EYE PROTEIN; OPSIN; PHOSPHODIESTERASE; PHOSPHODIESTERASE 6 DELTA SUBUNIT; PRENYL BINDING PROTEIN DELTA; REGULATOR PROTEIN; RETINITIS PIGMENTOSA GUANOSINE TRIPHOSPHATASE REGULATOR INTERACTING PROTEIN; RETINITIS PIGMENTOSA GUANOSINE TRIPHOSPHATASE REGULATOR PROTEIN; RHODOPSIN; UNCLASSIFIED DRUG; CARRIER PROTEIN; PHOSPHODIESTERASE VI; PROTEIN; RPGR PROTEIN, MOUSE; RPGRIP1 PROTEIN, MOUSE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BAGG ALBINO MOUSE; BREEDING; C57BL 6 MOUSE; CONTROLLED STUDY; ELECTRORETINOGRAPHY; EMBRYONIC STEM CELL; EXON; GENE DELETION; GENE TARGETING; HISTOPATHOLOGY; IMMUNOHISTOCHEMISTRY; IN FRAME DELETION; MALE; MOUSE; MOUSE MUTANT; NONHUMAN; NUCLEOTIDE SEQUENCE; OPEN READING FRAME; PHENOTYPIC VARIATION; PRIORITY JOURNAL; PROTEIN LOCALIZATION; REGULATOR GENE; RETINA CONE DISEASE; RETINA DISEASE; RETINA ROD DISEASE; RETINITIS PIGMENTOSA GUANOSINE TRIPHOSPHATASE REGULATOR GENE; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; STRAIN DIFFERENCE; TRANSGENIC MOUSE; WILD TYPE; ANIMAL; C57BL MOUSE; DISEASE MODEL; FEMALE; FLUORESCENT ANTIBODY TECHNIQUE; GENETICS; GENOTYPE; METABOLISM; MUTATION; PATHOPHYSIOLOGY; PHYSIOLOGY; RETINA CONE; RETINA ROD;

ANIMALS; CARRIER PROTEINS; CYCLIC NUCLEOTIDE PHOSPHODIESTERASES, TYPE 6; DISEASE MODELS, ANIMAL; ELECTRORETINOGRAPHY; EMBRYONIC STEM CELLS; EXONS; EYE PROTEINS; FEMALE; FLUORESCENT ANTIBODY TECHNIQUE, INDIRECT; GENOTYPE; MALE; MICE; MICE, INBRED BALB C; MICE, INBRED C57BL; MICE, TRANSGENIC; MUTATION; OPSINS; PROTEINS; RETINAL CONE PHOTORECEPTOR CELLS; RETINAL DISEASES; RETINAL ROD PHOTORECEPTOR CELLS; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RHODOPSIN;

EID: 77449151188     PISSN: 01460404     EISSN: 15525783     Source Type: Journal    
DOI: 10.1167/iovs.08-2742     Document Type: Article

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