Recent progress in the etiopathogenesis of pediatric biliary disease, particularly Caroli's disease with congenital hepatic fibrosis and biliary atresia

Histology and Histopathology

Volumn 25, Issue 2, 2010, Pages 223-235

  Nakanuma, Yasuni ^a   Harada, Kenichi ^a   Sato, Yasunori ^a   Ikeda, Hiroko ^b  

^a KANAZAWA UNIVERSITY GRADUATE SCHOOL OF MEDICAL SCIENCE   (Japan)

^b KANAZAWA UNIVERSITY HOSPITAL   (Japan)

Author keywords

Cystogenesis; Epithelial mesenchymal transition; Hepatic fibrosis; Innate immunity; Intrahepatic bile duct

Indexed keywords

SCLEROPROTEIN; SIGNAL PEPTIDE;

ADAPTIVE IMMUNITY; ANIMAL; BILE DUCT ATRESIA; CAROLI DISEASE; CONGENITAL MALFORMATION; DISEASE MODEL; GENETIC PREDISPOSITION; GENETICS; HUMAN; IMMUNOLOGY; INNATE IMMUNITY; INTRAHEPATIC BILE DUCT; KIDNEY POLYCYSTIC DISEASE; LESIONS AND DEFECTS; LIVER CIRRHOSIS; METABOLISM; MUTATION; PATHOLOGY; RAT; REVIEW; RISK FACTOR; T LYMPHOCYTE; VIRUS INFECTION;

ADAPTIVE IMMUNITY; ANIMALS; BILE DUCTS, INTRAHEPATIC; BILIARY ATRESIA; CAROLI DISEASE; DILATATION, PATHOLOGIC; DISEASE MODELS, ANIMAL; EXTRACELLULAR MATRIX PROTEINS; GENETIC PREDISPOSITION TO DISEASE; HUMANS; IMMUNITY, INNATE; INTERCELLULAR SIGNALING PEPTIDES AND PROTEINS; LIVER CIRRHOSIS; MUTATION; POLYCYSTIC KIDNEY DISEASES; RATS; RISK FACTORS; T-LYMPHOCYTES; VIRUS DISEASES;

ANIMALIA; RATTUS;

EID: 75149151621     PISSN: 02133911     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Review

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