Glanzmann's thrombasthenia (defective platelet integrin αIIb-β3): Proposals for management between evidence and open issues

Thrombosis and Haemostasis

Volumn 102, Issue 6, 2009, Pages 1157-1164

  Di Minno, Giovanni ^a   Coppola, Antonio ^a   Di Minno, Matteo N D ^a   Poon, Man Chiu ^b  

^a UNIVERSITY OF NAPLES FEDERICO II   (Italy)

^b UNIVERSITY OF CALGARY   (Canada)

Author keywords

Anti platelet antibodies; Clinical management; Glanzmann's thrombasthenia; Platelet transfusion; Recombinant activated factor VII

Indexed keywords

ALLOANTIBODY; ANTIFIBRINOLYTIC AGENT; BETA3 INTEGRIN; BLOOD CLOTTING FACTOR 7A; DESMOPRESSIN; THROMBOCYTE ANTIBODY; VERY LATE ACTIVATION ANTIGEN 2;

BLEEDING DISORDER; CLINICAL RESEARCH; CONSERVATIVE TREATMENT; DISEASE SEVERITY; GLANZMANN DISEASE; HORMONAL THERAPY; HUMAN; MAJOR SURGERY; MINOR SURGERY; PATIENT EDUCATION; PRIORITY JOURNAL; REVIEW; THROMBOCYTE ANOMALY; THROMBOCYTE TRANSFUSION;

ANTIFIBRINOLYTIC AGENTS; BLOOD PLATELETS; DEAMINO ARGININE VASOPRESSIN; EVIDENCE-BASED MEDICINE; FACTOR VIIA; FEMALE; HUMANS; MALE; PATIENT EDUCATION AS TOPIC; PLATELET GLYCOPROTEIN GPIIB-IIIA COMPLEX; PLATELET TRANSFUSION; PROGESTERONE; RECOMBINANT PROTEINS; THROMBASTHENIA;

EID: 72949116778     PISSN: 03406245     EISSN: None     Source Type: Journal    
DOI: 10.1160/TH-09-04-0225     Document Type: Review

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