Successful treatment of the murine model of cystinosis using bone marrow cell transplantation

Blood

Volumn 114, Issue 12, 2009, Pages 2542-2552

  Syres, Kimberly ^a   Harrison, Frank ^a   Tadlock, Matthew ^a   Jester, James V ^b   Simpson, Jennifer ^b   Roy, Subhojit ^c   Salomon, Daniel R ^a   Cherqui, Stephanie ^a  

^a SCRIPPS RESEARCH INSTITUTE   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CYSTINE; LUCIFERASE; MESSENGER RNA;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BONE MARROW TRANSPLANTATION; CELL COUNT; CELL LINEAGE; CONFOCAL MICROSCOPY; CONTROLLED STUDY; CORNEA; CYSTINOSIS; DISEASE MODEL; FEMALE; HEMATOPOIETIC STEM CELL TRANSPLANTATION; KIDNEY DYSFUNCTION; MALE; MESENCHYMAL STEM CELL TRANSPLANTATION; METABOLIC TRANSPORT DISORDER; MOUSE; NONHUMAN; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; PROTEIN CONTENT; PROTEIN LOCALIZATION; RENAL PROTECTION; THERAPY EFFECT; TREATMENT OUTCOME; ANIMAL; BLOOD; C57BL MOUSE; ENZYME IMMUNOASSAY; FLOW CYTOMETRY; FLUORESCENT ANTIBODY TECHNIQUE; GENETICS; MESENCHYMAL STEM CELL; METABOLISM; MOUSE MUTANT; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; TISSUE DISTRIBUTION; TRANSGENIC MOUSE; URINE; WESTERN BLOTTING;

ANIMALS; BLOTTING, WESTERN; BONE MARROW TRANSPLANTATION; CYSTINOSIS; DISEASE MODELS, ANIMAL; FLOW CYTOMETRY; FLUORESCENT ANTIBODY TECHNIQUE; HEMATOPOIETIC STEM CELL TRANSPLANTATION; IMMUNOENZYME TECHNIQUES; LUCIFERASES; MESENCHYMAL STEM CELLS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MICE, TRANSGENIC; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RNA, MESSENGER; TISSUE DISTRIBUTION;

EID: 70350509583     PISSN: 00064971     EISSN: 15280020     Source Type: Journal    
DOI: 10.1182/blood-2009-03-213934     Document Type: Article

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