Cor pulmonale due to congenital central hypoventilation syndrome presenting in adolescence

Pediatric Critical Care Medicine

Volumn 10, Issue 4, 2009, Pages

  Fine Goulden, Miriam R ^a   Manna, Soumendu ^a   Durward, Andrew ^a  

^a EVELINA LONDON CHILDREN S HOSPITAL   (United Kingdom)

Author keywords

Congenital central hypoventilation syndrome; Cor pulmonale; PHOX2B

Indexed keywords

ALANINE; BICARBONATE; DIURETIC AGENT; FENTANYL; HEMOGLOBIN; MORPHINE;

AMINO ACID SUBSTITUTION; APNEA; ARTICLE; ARTIFICIAL VENTILATION; BICARBONATE BLOOD LEVEL; CASE REPORT; CHILD; COR PULMONALE; DAYTIME SOMNOLENCE; ELECTROCARDIOGRAM; FEMALE; GENE MUTATION; HEART RIGHT VENTRICLE FAILURE; HETEROZYGOTE; HUMAN; HYPERCAPNIA; HYPOVENTILATION; HYPOXIA; INTENSIVE CARE UNIT; INTUBATION; NUCLEOTIDE REPEAT; PEDIATRIC HOSPITAL; POLYCYTHEMIA; POLYMERASE CHAIN REACTION; POSITIVE END EXPIRATORY PRESSURE; PRIORITY JOURNAL; SCHOOL CHILD; SEDATION; TERTIARY HEALTH CARE; TOOTH EXTRACTION; TRACHEOSTOMY; TREATMENT OUTCOME; TREATMENT RESPONSE;

EID: 70349286776     PISSN: 15297535     EISSN: None     Source Type: Journal    
DOI: 10.1097/PCC.0b013e318198b219     Document Type: Article

References (7)

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