Vagal and sympathetic heart rate and blood pressure control in adult onset PHOX2B mutation-confirmed congenital central hypoventilation syndrome

Clinical Autonomic Research

Volumn 17, Issue 3, 2007, Pages 177-185

  Diedrich, André ^a   Malow, Beth A ^a,b   Antic, Nick A ^c   Sato, Kyoko ^a   McEvoy, R Doug ^c   Mathias, Christopher J ^d,e   Robertson, David ^a   Berry Kravis, Elizabeth M ^f   Weese Mayer, Debra E ^f  

^a VANDERBILT UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b VANDERBILT UNIVERSITY MEDICAL CENTER   (United States)

^c REPATRIATION GENERAL HOSPITAL   (Australia)

^d NATIONAL HOSPITAL FOR NEUROLOGY AND NEUROSURGERY   (United Kingdom)

^e ST MARY S HOSPITAL   (United Kingdom)

^f RUSH UNIVERSITY MEDICAL CENTER   (United States)

Author keywords

Autonomic nervous system; Baroreflex; Blood pressure variability; Congenital central hypoventilation syndrome; Heart rate variability; Muscle; PHOX2B; Sympathetic activity

Indexed keywords

TRANSCRIPTION FACTOR; TRANSCRIPTION FACTOR PHOX2B; UNCLASSIFIED DRUG;

ADULT; ADULTHOOD; ARTICLE; AUTONOMIC DYSFUNCTION; AUTONOMIC NERVOUS SYSTEM FUNCTION; BLOOD PRESSURE REGULATION; BLOOD PRESSURE VARIABILITY; CARDIOVASCULAR PARAMETERS; CARDIOVASCULAR RESPONSE; CAROTID BODY; CLINICAL ARTICLE; COLD PRESSOR TEST; CONTROLLED STUDY; FEMALE; GENE MUTATION; GENOTYPE; HEART RATE VARIABILITY; HUMAN; HYPOXEMIA; ISOMETRIC EXERCISE; LUNG ALVEOLUS HYPOVENTILATION; MALE; MUSCLE FUNCTION; ONSET AGE; PRESSORECEPTOR REFLEX; SENSORY GANGLION; SYMPATHETIC FUNCTION; VAGUS REFLEX; VALSALVA MANEUVER;

ADULT; BAROREFLEX; BLOOD PRESSURE; CATECHOLAMINES; FEMALE; GENOTYPE; HEART FUNCTION TESTS; HEART RATE; HOMEODOMAIN PROTEINS; HUMANS; MUTATION; RESPIRATORY FUNCTION TESTS; SLEEP APNEA, CENTRAL; SYMPATHETIC NERVOUS SYSTEM; SYNDROME; TRANSCRIPTION FACTORS; VAGUS NERVE;

EID: 34447103985     PISSN: 09599851     EISSN: None     Source Type: Journal    
DOI: 10.1007/s10286-007-0421-4     Document Type: Article

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