Selective occurrence of TDP-43-immunoreactive inclusions in the lower motor neurons in Machado - Joseph disease

Acta Neuropathologica

Volumn 118, Issue 4, 2009, Pages 553-560

  Tan, Chun Feng ^a   Yamada, Mitsunori ^a,b   Toyoshima, Yasuko ^a   Yokoseki, Akio ^a   Miki, Yukari ^a   Hoshi, Yasuhiro ^a   Kaneko, Hiroyuki ^a   Ikeuchi, Takeshi ^a   Onodera, Osamu ^a   Kakita, Akiyoshi ^a   Takahashi, Hitoshi ^a  

^a NIIGATA UNIVERSITY   (Japan)

^b National Saigata Medical Center   (Japan)

Author keywords

Amyotrophic lateral sclerosis; Lower motor neuron; Machado Joseph disease; Neuronal cytoplasmic inclusion; TDP 43

Indexed keywords

ATAXIN 3; CYSTEINYLALANYLGLYCINE; PHOSPHOSERINE; POLYCLONAL ANTIBODY; POLYGLUTAMINE; TAR DNA BINDING PROTEIN; TRIPEPTIDE; UBIQUITIN; UNCLASSIFIED DRUG;

ADULT; AGED; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; BRAIN STEM; CELL INCLUSION; CELL SHAPE; CELL ULTRASTRUCTURE; CLINICAL ARTICLE; CONTROLLED STUDY; DEGENERATIVE DISEASE; FEMALE; HUMAN; HUMAN TISSUE; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; IMMUNOREACTIVITY; KENNEDY DISEASE; MACHADO JOSEPH DISEASE; MALE; MOTONEURON; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN LOCALIZATION; PROTEIN PHOSPHORYLATION; SPINAL CORD;

ADULT; AGED; AGED, 80 AND OVER; BLOTTING, WESTERN; BRAIN; CELL DEATH; DNA-BINDING PROTEINS; FEMALE; FLUORESCENT ANTIBODY TECHNIQUE; HUMANS; IMMUNOHISTOCHEMISTRY; INCLUSION BODIES; MACHADO-JOSEPH DISEASE; MALE; MICROSCOPY, IMMUNOELECTRON; MIDDLE AGED; MOTOR NEURONS; MUSCULAR ATROPHY, SPINAL; SPINAL CORD;

EID: 69949174325     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-009-0552-x     Document Type: Article

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