Impaired expression of ciliary neurotrophic factor in Charcot-Marie-Tooth type 1A neuropathy

Journal of Neuropathology and Experimental Neurology

Volumn 68, Issue 5, 2009, Pages 441-455

  Nobbio, Lucilla ^a   Fiorese, Fulvia ^a   Vigo, Tiziana ^a   Cilli, Michele ^b   Gherardi, Gianfranco ^a   Grandis, Marina ^a   Melcangi, Roberto Cosimo ^c   Mancardi, Gianluigi ^a   Abbruzzese, Michele ^a   Schenone, Angelo ^a  

^a UNIVERSITY OF GENOA   (Italy)

^b UNIVERSITY OF GENOA   (Italy)

^c UNIVERSITY OF MILAN   (Italy)

Author keywords

Axonal impairment; Charcot Marie Tooth; Ciliary neurotrophic factor (CNTF); CMT1A; Demyelination; DRG cultures; Neuroprotection; Peripheral myelin protein 22 (PMP22); Schwann cells (SCs)

Indexed keywords

AMYLOID PRECURSOR PROTEIN; CILIARY NEUROTROPHIC FACTOR; NEUROFILAMENT PROTEIN; GLIAL FIBRILLARY ACIDIC PROTEIN; MYELIN PROTEIN; PMP22 PROTEIN, RAT; STAT3 PROTEIN;

AGING; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL CULTURE; CHARCOT MARIE TOOTH TYPE 1A NEUROPATHY; CONTROLLED STUDY; DEMYELINATION; DISEASE COURSE; GENE EXPRESSION; HEREDITARY MOTOR SENSORY NEUROPATHY; HUMAN; NERVE FIBER DEGENERATION; NEUROFILAMENT; NEUROPATHY; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN DEPHOSPHORYLATION; PROTEIN PHOSPHORYLATION; RAT; SCHWANN CELL; SCIATIC NERVE; SPINAL GANGLION; AGE; ANALYSIS OF VARIANCE; ANIMAL; ANIMAL EMBRYO; BIOPSY; CYTOLOGY; DISEASE MODEL; DRUG EFFECT; ENZYME LINKED IMMUNOSORBENT ASSAY; GENE EXPRESSION REGULATION; GENETICS; MALE; METABOLISM; METHODOLOGY; MIDDLE AGED; MOUSE; MOUSE MUTANT; NERVE FIBER; NEWBORN; PATHOLOGY; PHYSIOLOGY; SCIATIC NEUROPATHY; TIME; TRANSGENIC RAT;

AGE FACTORS; AMYLOID BETA-PROTEIN PRECURSOR; ANALYSIS OF VARIANCE; ANIMALS; ANIMALS, NEWBORN; AXONS; BIOPSY; CELLS, CULTURED; CHARCOT-MARIE-TOOTH DISEASE; CILIARY NEUROTROPHIC FACTOR; DISEASE MODELS, ANIMAL; EMBRYO, MAMMALIAN; ENZYME-LINKED IMMUNOSORBENT ASSAY; GANGLIA, SPINAL; GENE EXPRESSION REGULATION; GLIAL FIBRILLARY ACIDIC PROTEIN; HUMANS; MALE; MICE; MICE, KNOCKOUT; MIDDLE AGED; MYELIN PROTEINS; NEUROFILAMENT PROTEINS; RATS; RATS, TRANSGENIC; SCHWANN CELLS; SCIATIC NERVE; SCIATIC NEUROPATHY; STAT3 TRANSCRIPTION FACTOR; TIME FACTORS;

EID: 69249140104     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1097/NEN.0b013e31819fa6ba     Document Type: Article

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