-
1
-
-
0019809960
-
Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis
-
Knowles M, Gatzy J, Boucher R. Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis. N Engl J Med 1981;305:1489-1495. (Pubitemid 12244203)
-
(1981)
New England Journal of Medicine
, vol.305
, Issue.25
, pp. 1489-1495
-
-
Knowles, M.1
Gatzy, J.2
Boucher, R.3
-
2
-
-
44949253090
-
Nasal potential difference in non-classic cystic fibrosis - Long term follow up
-
DOI 10.1002/ppul.20807
-
Jaron R, Yaakov Y, Rivlin J, Blau H, Bentur L, Yahav Y, Kerem E, Bibi H, Picard E, Wilschanski M. Nasal potential difference in non-classic cystic fibrosis - long term follow up. Pediatr Pulmonol 2008;43:545-549. (Pubitemid 351813007)
-
(2008)
Pediatric Pulmonology
, vol.43
, Issue.6
, pp. 545-549
-
-
Jaron, R.1
Yaakov, Y.2
Rivlin, J.3
Blau, H.4
Bentur, L.5
Yahav, Y.6
Kerem, E.7
Bibi, H.8
Picard, E.9
Wilschanski, M.10
-
3
-
-
0028020058
-
Protocols for in vivo measurement of the ion transport defects in cystic fibrosis nasal epithelium
-
Middleton PG, Geddes DM, Alton EWFW. Protocols for in vivo measurement of the ion transport defects in cystic fibrosis nasal epithelium. Eur Respir J 1994;7:2050-2056. (Pubitemid 24366300)
-
(1994)
European Respiratory Journal
, vol.7
, Issue.11
, pp. 2050-2056
-
-
Middleton, P.G.1
Geddes, D.M.2
Alton, E.W.F.W.3
-
4
-
-
0034961206
-
Hypertonic saline alters ion transport across the human airway epithelium
-
DOI 10.1183/09031936.01.17201950
-
Middleton PG, Pollard KA, Wheatley JR. Hypertonic saline alters ion transport across the normal airway epithelium. Eur Respir J 2001;17:195-199. (Pubitemid 32600577)
-
(2001)
European Respiratory Journal
, vol.17
, Issue.2
, pp. 195-199
-
-
Middleton, P.G.1
Pollard, K.A.2
Wheatley, J.R.3
-
5
-
-
0032615611
-
The in vivo effects of milrinone on the airways of cystic fibrosis mice and human subjects
-
Smith SN, Middleton PG, Chadwick S, Jaffe A, Bush KA, Rolleston S, Farley R, Delaney SJ, Wainwright B, Geddes DM, Alton EWFW, The in vivo effects of milrinone on the airways of cystic fibrosis mice and human subjects. Am J Respir Cell Mol Biol 1999;20:129-134. (Pubitemid 129504851)
-
(1999)
American Journal of Respiratory Cell and Molecular Biology
, vol.20
, Issue.1
, pp. 129-134
-
-
Smith, S.N.1
Middleton, P.G.2
Chadwick, S.3
Jaffe, A.4
Bush, K.A.5
Rolleston, S.6
Farley, R.7
Delaney, S.J.8
Wainwright, B.9
Geddes, D.M.10
Alton, E.W.F.W.11
-
6
-
-
0028991826
-
In vivo nasal potential difference: Techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis
-
Knowles MR, Paradiso AM, Boucher RC. In vivo nasal potential difference: techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis. Hum Gene Ther 1995;6:445-455.
-
(1995)
Hum Gene Ther
, vol.6
, pp. 445-455
-
-
Knowles, M.R.1
Paradiso, A.M.2
Boucher, R.C.3
-
7
-
-
0034821606
-
A modified technique for measurement of nasal transepithelial potential difference in infants
-
DOI 10.1067/mpd.2001.116278
-
Southern KW, Noone PG, Bosworth DG, Legrys VA, Knowles MR, Barker PM. A modified technique for measurement of nasal transepithelial potential difference in infants. J Pediatr 2001;139: 353-358. (Pubitemid 32889510)
-
(2001)
Journal of Pediatrics
, vol.139
, Issue.3
, pp. 353-358
-
-
Southern, K.W.1
Noone, P.G.2
Bosworth, D.G.3
Legrys, V.A.4
Knowles, M.R.5
Barker, P.M.6
-
8
-
-
0034073736
-
A pilot study of the effect of gentamicin on nasal potential difference measurements in cystic fibrosis patients carrying stop mutations
-
Wilschanski M, Famini C, Blau H, Rivlin J, Augarten A, Avital A, Kerem B, Kerem E. A pilot study of the effect of gentamicin on nasal potential difference measurements in cystic fibrosis patients carrying stop mutations. Am J Respir Crit Care Med 2000;161: 860-865. (Pubitemid 30171743)
-
(2000)
American Journal of Respiratory and Critical Care Medicine
, vol.161
, Issue.3 I
, pp. 860-865
-
-
Wilschanski, M.1
Famini, C.2
Blau, H.3
Rivlin, J.4
Augarten, A.5
Avital, A.6
Kerem, B.7
Kerem, E.8
-
9
-
-
50149098401
-
Effectiveness of PTC124 treatment of cystic fibrosis caused by nonsense mutations: A prospective phase II trial
-
Kerem E, Hirawat S, Armoni S, Yaakov Y, Shoseyov D, Cohen M, Nissim-Rafinia M, Blau H, Rivlin J, Aviram M, Elfring GL, Northcutt VJ, Miller LL, Kerem B, Wilschanski M. Effectiveness of PTC124 treatment of cystic fibrosis caused by nonsense mutations: a prospective phase II trial. Lancet 2008;372:719-727.
-
(2008)
Lancet
, vol.372
, pp. 719-727
-
-
Kerem, E.1
Hirawat, S.2
Armoni, S.3
Yaakov, Y.4
Shoseyov, D.5
Cohen, M.6
Nissim-Rafinia, M.7
Blau, H.8
Rivlin, J.9
Aviram, M.10
Elfring, G.L.11
Northcutt, V.J.12
Miller, L.L.13
Kerem, B.14
Wilschanski, M.15
-
10
-
-
2442453783
-
Standardized Procedure for Measurement of Nasal Potential Difference: An Outcome Measure in Multicenter Cystic Fibrosis Clinical Trials
-
DOI 10.1002/ppul.10448
-
Standaert TA, Boitano L, Emerson J, Milgram LJ, Konstan MW, Hunter J, Berclaz PY, Brass L, Zeitlin PL, Hammond K, Davies Z, Foy C, Noone PG, Knowles MR. Standardized procedure for measurement of nasal potential difference: an outcome measure in multicenter cystic fibrosis clinical trials. Pediatr Pulmonol 2004;37:385-392. (Pubitemid 38620059)
-
(2004)
Pediatric Pulmonology
, vol.37
, Issue.5
, pp. 385-392
-
-
Standaert, T.A.1
Boitano, L.2
Emerson, J.3
Milgram, L.J.H.4
Konstan, M.W.5
Hunter, J.6
Berclaz, P.-Y.7
Brass, L.8
Zeitlin, P.L.9
Hammond, K.10
Davies, Z.11
Foy, C.12
Noone, P.G.13
Knowles, M.R.14
-
11
-
-
0043234162
-
A multicenter study of the effect of solution temperature on nasal potential difference measurements
-
DOI 10.1378/chest.124.2.482
-
Boyle MP, Diener-West M, Milgram L, Knowles MR, Foy C, Zeitlin PL, Standaert TA. A multicenter study of the effect of solution temperature on nasal potential difference measurements. Chest 2003;124:482-489. (Pubitemid 37000123)
-
(2003)
Chest
, vol.124
, Issue.2
, pp. 482-489
-
-
Boyle, M.P.1
Diener-West, M.2
Milgram, L.3
Knowles, M.4
Foy, C.5
Zeitlin, P.6
Standaert, T.7
-
12
-
-
0028230613
-
Nasal application of the cationic liposome DC-Chol:DOPE does not alter ion transport, lung function or bacterial growth
-
Middleton PG, Caplen NJ, Gao X, Huang L, Gaya H, Geddes DM, Alton EWFW. Nasal application of the cationic liposome DC-Chol:DOPE does not alter ion transport, lung function or bacterial growth. Eur Respir J 1994;7:442-445. (Pubitemid 24099002)
-
(1994)
European Respiratory Journal
, vol.7
, Issue.3
, pp. 442-445
-
-
Middleton, P.G.1
Caplen, N.J.2
Gao, X.3
Huang, L.4
Gaya, H.5
Geddes, D.M.6
Alton, E.W.F.W.7
-
13
-
-
0242468630
-
Airway Surface Liquid Calcium Modulates Chloride Permeability in the Cystic Fibrosis Airway
-
DOI 10.1164/rccm.200305-628OC
-
Middleton PG, Pollard KA, Donohoo E, Wheatley JR, Geddes DM, Alton EWFW. Airway surface liquid calcium modulates chloride permeability in the cystic fibrosis airway. Am J Respir Crit Care Med 2003;168:1223-1226. (Pubitemid 37421840)
-
(2003)
American Journal of Respiratory and Critical Care Medicine
, vol.168
, Issue.10
, pp. 1223-1226
-
-
Middleton, P.G.1
Pollard, K.A.2
Donohoo, E.3
Wheatley, J.R.4
Geddes, D.M.5
Alton, E.W.6
-
14
-
-
33947118871
-
Airway glucose concentrations and effect on growth of respiratory pathogens in cystic fibrosis
-
DOI 10.1016/j.jcf.2006.03.009, PII S1569199306000932
-
Brennan AL, Gyi KM,Wood DM, Johnson J, Holliman R, Baines DL, Philips BJ, Geddes DM, Hodson ME, Baker EH. Airway glucose concentrations and effect on growth of respiratory pathogens in cystic fibrosis. J Cystic Fibros 2007;6:101-109. (Pubitemid 46394299)
-
(2007)
Journal of Cystic Fibrosis
, vol.6
, Issue.2
, pp. 101-109
-
-
Brennan, A.L.1
Gyi, K.M.2
Wood, D.M.3
Johnson, J.4
Holliman, R.5
Baines, D.L.6
Philips, B.J.7
Geddes, D.M.8
Hodson, M.E.9
Baker, E.H.10
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