An unusual clinical presentation of factor XIII deficiency and issues relating to the monitoring of factor XIII replacement therapy

Blood Coagulation and Fibrinolysis

Volumn 19, Issue 5, 2008, Pages 447-452

  Dargaud, Yesim ^a,b   De Mazancourt, Philippe ^c   Rugeri, Lucia ^a   Hanss, Michel ^d   Borg, Jeanne Yvonne ^e   Gaucherand, Pascal ^a   Negrier, Claude ^a,b   Trzeciak, Christine ^a  

^a EDOUARD HERRIOT HOSPITAL   (France)

^b University Lyon 1   (France)

^c RAYMOND POINCARÉ HOSPITAL   (France)

^d LOUIS PRADEL HOSPITAL   (France)

^e HÔPITAL CHARLES NICOLLE   (France)

Author keywords

Dysfunctional factor XIII; Factor XIII deficiency; G 501 R mutation; Miscarriages; Thromboelastometry

Indexed keywords

BLOOD CLOTTING FACTOR 13; BLOOD CLOTTING FACTOR 13 CONCENTRATE; BLOOD CLOTTING FACTOR 5; FRESH FROZEN PLASMA; NADROPARIN;

ADULT; ANAMNESIS; ARTICLE; BLOOD CLOTTING FACTOR 13 DEFICIENCY; CASE REPORT; CHILDHOOD DISEASE; CLINICAL FEATURE; DISEASE SEVERITY; DISSEMINATED INTRAVASCULAR CLOTTING; DRUG INFUSION; FEMALE; FETUS WASTAGE; GENE MUTATION; HETEROZYGOSITY; HIGH RISK PATIENT; HOMOZYGOSITY; HUMAN; PREGNANCY; PRIORITY JOURNAL; RECURRENT DISEASE; SPONTANEOUS ABORTION; THROMBOSIS; UTERINE ARTERY EMBOLIZATION; UTERINE CERVIX INCOMPETENCE;

ABORTION, HABITUAL; ADULT; FACTOR XIII; FACTOR XIII DEFICIENCY; FEMALE; HUMANS; MONITORING, PHYSIOLOGIC; MUTATION, MISSENSE; PREGNANCY; THROMBELASTOGRAPHY;

EID: 67649553799     PISSN: 09575235     EISSN: None     Source Type: Journal    
DOI: 10.1097/MBC.0b013e328300c7ff     Document Type: Article

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