Renal disease associated with inherited disorders of the complement system

Pediatric Nephrology

Volumn 24, Issue 8, 2009, Pages 1439-1444

  Welch, Thomas R ^a   Blystone, Lisa W ^a  

^a State University of New York Upstate Medical University: College of Medicine   (United States)

Author keywords

Autoimmune disease; Complement; Deficiency; Genetics; Glomerulonephritis; Lupus erythematosus

Indexed keywords

ALTERNATIVE COMPLEMENT PATHWAY C3 C5 CONVERTASE; COMPLEMENT COMPONENT C1Q; COMPLEMENT COMPONENT C1R; COMPLEMENT COMPONENT C1S; COMPLEMENT COMPONENT C1S INHIBITOR; COMPLEMENT COMPONENT C2; COMPLEMENT COMPONENT C3; COMPLEMENT COMPONENT C3B RECEPTOR; COMPLEMENT COMPONENT C4A; COMPLEMENT COMPONENT C4B; COMPLEMENT COMPONENT C5; COMPLEMENT COMPONENT C7; COMPLEMENT COMPONENT C9; COMPLEMENT FACTOR D; COMPLEMENT FACTOR H; COMPLEMENT FACTOR I; MANNOSE BINDING LECTIN; MEMBRANE COFACTOR PROTEIN; NEPHRITIC FACTOR;

ANGIONEUROTIC EDEMA; AUTOIMMUNE DISEASE; CHROMOSOME 6P; COMPLEMENT ALTERNATIVE PATHWAY; COMPLEMENT CLASSICAL PATHWAY; COMPLEMENT DEFICIENCY; COMPLEMENT LECTIN PATHWAY; COMPLEMENT SYSTEM; DISEASE ASSOCIATION; FAMILIAL DISEASE; FOCAL GLOMERULOSCLEROSIS; GENE DELETION; GENE DUPLICATION; GENE MUTATION; HEMOLYTIC UREMIC SYNDROME; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HEREDITY; HUMAN; KIDNEY DISEASE; KIDNEY FAILURE; LUPUS ERYTHEMATOSUS NEPHRITIS; MAJOR HISTOCOMPATIBILITY COMPLEX; MEMBRANOPROLIFERATIVE GLOMERULONEPHRITIS; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL; REVIEW; SYSTEMIC LUPUS ERYTHEMATOSUS;

CHILD; COMPLEMENT PATHWAY, CLASSICAL; COMPLEMENT SYSTEM PROTEINS; HUMANS; IMMUNE SYSTEM DISEASES; KIDNEY DISEASES;

EID: 67649389597     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-008-1027-3     Document Type: Review

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