Mucolipidosis type IV: The effect of increased lysosomal ph on the abnormal lysosomal storage

Pediatric Research

Volumn 65, Issue 6, 2009, Pages 686-690

  Kogot Levin, Aviram ^a   Zeigler, Marsha ^a   Ornoy, Asher ^a   Bach, Gideon ^a  

^a HADASSAH HEBREW UNIVERSITY MEDICAL CENTER   (Israel)

Author keywords

[No Author keywords available]

Indexed keywords

CALCIUM CHANNEL; CHLOROQUINE; COMPLEMENTARY DNA; MEMBRANE PROTEIN; NIGERICIN; PROTEIN TRPML1; TRANSIENT RECEPTOR POTENTIAL CHANNEL 1; UNCLASSIFIED DRUG;

ARTICLE; CATION TRANSPORT; CONTROLLED STUDY; ENDOSOME; FIBROBLAST CULTURE; GENE; HUMAN; HUMAN CELL; HUMAN TISSUE; LYSOSOME; LYSOSOME MEMBRANE; LYSOSOME STORAGE DISEASE; MCOLN1 GENE; MEMBRANE ELECTROPHYSIOLOGY; MEMBRANE VESICLE; MUCOLIPIDOSIS; MUCOLIPIDOSIS TYPE 4; PH MEASUREMENT; PRIORITY JOURNAL; PROTEIN LOCALIZATION; PROTON TRANSPORT;

ANTIMALARIALS; CELLS, CULTURED; CHLOROQUINE; FIBROBLASTS; HUMANS; HYDROGEN-ION CONCENTRATION; IONOPHORES; LYSOSOMES; MUCOLIPIDOSES; NIGERICIN; TRPM CATION CHANNELS;

EID: 67049154111     PISSN: 00313998     EISSN: 15300447     Source Type: Journal    
DOI: 10.1203/PDR.0b013e3181a1681a     Document Type: Article

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