Sporadic amyotrophic lateral sclerosis: Widespread multisystem degeneration with TDP-43 pathology in a patient after long-term survival on a respirator: Case report

Neuropathology

Volumn 29, Issue 6, 2009, Pages 689-696

  Nishihira, Yasushi ^a   Tan, Chun Feng ^a   Toyoshima, Yasuko ^a   Yonemochi, Yosuke ^b   Kondo, Hiroshi ^c   Nakajima, Takashi ^b   Takahashi, Hitoshi ^a  

^a NIIGATA UNIVERSITY   (Japan)

^b Niigata National Hospital   (Japan)

^c National Hospital Organization   (Japan)

Author keywords

Artificial respiratory support; Long term survival; Sporadic amyotrophic lateral sclerosis; TDP 43; Ubiquitin

Indexed keywords

TAR DNA BINDING PROTEIN; UBIQUITIN;

AGED; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; ARTIFICIAL VENTILATION; ASPIRATION PNEUMONIA; AUTOPSY; BRAIN ATROPHY; BRAIN ELECTROPHYSIOLOGY; BRAIN STEM; CASE REPORT; COMPUTER ASSISTED TOMOGRAPHY; CYTOPLASM; DISEASE COURSE; DISEASE DURATION; DYSPHAGIA; DYSPNEA; FEMALE; FRONTAL LOBE; HUMAN; HUMAN TISSUE; IMMUNOFLUORESCENCE; IMMUNOREACTIVITY; LEWY BODY; MOTONEURON; MOTONEURON NUCLEUS; MUSCLE WEAKNESS; NERVE DEGENERATION; NERVOUS SYSTEM; NEUROPATHOLOGY; PNEUMONIA; PRIORITY JOURNAL; SURVIVAL TIME; TEGMENTUM; TENDON REFLEX; UBIQUITINATION; URINARY TRACT INFECTION; VENTILATED PATIENT; VENTILATOR;

AGED; AMYOTROPHIC LATERAL SCLEROSIS; ATROPHY; BRAIN; DNA-BINDING PROTEINS; FEMALE; FLUORESCENT ANTIBODY TECHNIQUE; HUMANS; INCLUSION BODIES; MOTOR NEURONS; RESPIRATION, ARTIFICIAL;

EID: 65149090786     PISSN: 09196544     EISSN: 14401789     Source Type: Journal    
DOI: 10.1111/j.1440-1789.2008.00999.x     Document Type: Article

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