Alfa-1-antitrypsin deficiency panniculitis acquired after liver transplant and successfully treated with retransplant

Journal of the American Academy of Dermatology

Volumn 60, Issue 4, 2009, Pages 715-716

  Fernández Torres, Rosa ^a   García Silva, Jesús ^a   Robles, Olga ^a   Otero, Alejandra ^a   Vázquez, María Ángeles ^a   Fonseca, Eduardo ^a  

^a HOSPITAL JUAN CANALEJO   (Spain)

Author keywords

[No Author keywords available]

Indexed keywords

AZATHIOPRINE; CYCLOSPORIN; PREDNISONE; TRYPSIN INHIBITOR;

ADULT; ALCOHOL LIVER CIRRHOSIS; ALPHA ANTITRYPSIN DEFICIENCY; ARTICLE; CASE REPORT; HUMAN; HUMAN TISSUE; IMMUNOSUPPRESSIVE TREATMENT; LIVER GRAFT; LIVER GRAFT REJECTION; MALE; PANNICULITIS; PHENOTYPE; PHYSICAL EXAMINATION; PRIORITY JOURNAL; SKIN BIOPSY;

ALPHA 1-ANTITRYPSIN DEFICIENCY; HUMANS; LIVER TRANSPLANTATION; MALE; MIDDLE AGED; PANNICULITIS; POSTOPERATIVE COMPLICATIONS; RETREATMENT;

EID: 61849149365     PISSN: 01909622     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jaad.2008.10.012     Document Type: Article

References (5)

1. 1-Antitrypsin deficiency, emphysema and liver disease: genetics and strategies for therapy. J Clin Invest 85 (1990) 1343-1352
2. Needham M., and Stockley R.A. Alpha 1-antitrypsin deficiency. 3: Clinical manifestations and natural history. Thorax 59 (2004) 441-445
3. Chowdhury M.M., Williams E.J., Morris J.S., Ferguson B.J., McGregor A.D., Hedges A.R., et al. Severe panniculitis caused by homozygous ZZ alpha 1-antitrypsin deficiency treated successfully with human purified enzyme. (Prolastin). Br J Dermatol 147 (2002) 1258-1261
4. Ortiz P.G., Skov B.G., and Benfeldt E. Alpha 1-antitrypsin deficiency-associated panniculitis: case report and review of treatment options. J Eur Acad Dermatol Venereol 19 (2005) 487-490
5. O'Riordan K., Blei A., Rao M.S., and Abecassis M. Alpha 1-antitrypsin deficiency-associated panniculitis: resolution with intravenous alpha 1-antitrypsin administration and liver transplantation. Transplantation 63 (1997) 480-482