Severe panniculitis caused by homozygous ZZ α1-antitrypsin deficiency treated successfully with human purified enzyme (Prolastin®)

British Journal of Dermatology

Volumn 147, Issue 6, 2002, Pages 1258-1261

  Chowdhury, M M U ^a   Williams, E J ^b   Morris, J S ^b   Ferguson, B J M ^b   McGregor, A D ^c   Hedges, A R ^b   Stamatakis, J D ^b   Pope, F M ^b,d  

^a UNIVERSITY HOSPITAL OF WALES   (United Kingdom)

^b PRINCESS OF WALES HOSPITAL   (United Kingdom)

^c MORRISTON HOSPITAL   (United Kingdom)

^d WEST MIDDLESEX UNIVERSITY HOSPITAL   (United Kingdom)

Author keywords

1 antitrypsin deficiency; Panniculitis; Prolastin ; ZZ homozygous

Indexed keywords

ALPHA 1 ANTITRYPSIN; ALPHA TOCOPHEROL; DAPSONE; DOXYCYCLINE; FRESH FROZEN PLASMA; HEPATITIS B VACCINE; HYDROCORTISONE; HYDROXYCHLOROQUINE; LUGOL; PREDNISOLONE;

ADULT; ALPHA 1 ANTITRYPSIN DEFICIENCY; ARTICLE; CASE REPORT; CLINICAL FEATURE; DISEASE ACTIVITY; DISEASE COURSE; DISEASE SEVERITY; DRUG EFFICACY; EUROPE; FEMALE; HEPATITIS B; HISTOPATHOLOGY; HOMOZYGOSITY; HUMAN; HUMAN TISSUE; PANNICULITIS; PHENOTYPE; PRIORITY JOURNAL; SKIN NECROSIS; TREATMENT OUTCOME; GENETICS; HOMOZYGOTE; PEDIGREE;

ADULT; ALPHA 1-ANTITRYPSIN; ALPHA 1-ANTITRYPSIN DEFICIENCY; FEMALE; HOMOZYGOTE; HUMANS; PANNICULITIS; PEDIGREE;

EID: 0036887247     PISSN: 00070963     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1365-2133.2002.05095.x     Document Type: Article

References (6)

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