Arrhythmogenic right ventricular cardiomyopathy/dysplasia: A not so rare "disease of the desmosome" with multiple clinical presentations

Clinical Research in Cardiology

Volumn 98, Issue 3, 2009, Pages 141-158

  Herren, Thomas ^a   Gerber, Philipp A ^a   Duru, Firat ^b  

^a Limmattal Hospital   (Switzerland)

^b UNIVERSITY HOSPITAL ZURICH   (Switzerland)

Author keywords

Cardiomyopathy; Desmosome; Exercise; Heart failure; ICD; Right ventricle; Sudden death

Indexed keywords

AMIODARONE; ANTICOAGULANT AGENT; BETA ADRENERGIC RECEPTOR BLOCKING AGENT; DESMOCOLLIN; DESMOGLEIN 2; DESMOPLAKIN; DIPEPTIDYL CARBOXYPEPTIDASE INHIBITOR; DIURETIC AGENT; MEMBRANE PROTEIN; PLAKOGLOBIN; PLAKOPHILIN; RYANODINE RECEPTOR 2; SOTALOL; TRANSFORMING GROWTH FACTOR BETA3; TRANSMEMBRANE PROTEIN 43; UNCLASSIFIED DRUG;

CLINICAL FEATURE; DEFIBRILLATOR; DESMOSOME; GENE MUTATION; HEART FAILURE; HEART RIGHT VENTRICLE DYSPLASIA; HEART VENTRICLE ARRHYTHMIA; HUMAN; PROGNOSIS; REVIEW;

ANIMALS; ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; CATHETER ABLATION; DEATH, SUDDEN, CARDIAC; DEFIBRILLATORS, IMPLANTABLE; DIAGNOSIS, DIFFERENTIAL; ELECTROCARDIOGRAPHY; HUMANS; MASS SCREENING; MUTATION; RISK FACTORS;

EID: 61349136209     PISSN: 18610684     EISSN: 18610692     Source Type: Journal    
DOI: 10.1007/s00392-009-0751-4     Document Type: Review

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