Liver disease associated with ZZ α1-antitrypsin deficiency and ursodeoxycholic acid therapy in children

Journal of Pediatric Gastroenterology and Nutrition

Volumn 47, Issue 5, 2008, Pages 623-629

  Lykavieris, Panayotis ^a   Ducot, Béatrice ^b   Lachaux, Alain ^c   Dabadie, Alain ^d   Broué, Pierre ^e   Sarles, Jacques ^f   Bernard, Olivier ^a   Jacquemin, Emmanuel ^a  

^a BICÊTRE HOSPITAL   (France)

^b INSERM   (France)

^c EDOUARD HERRIOT HOSPITAL   (France)

^d SERVICE DE RHUMATOLOGIE   (France)

^e HÔPITAL DES ENFANTS   (France)

^f TIMONE HOSPITAL   (France)

Author keywords

; antitrypsin deficiency; Children; Cholestasis; Liver disease; Ursodeoxycholic acid

Indexed keywords

ALANINE AMINOTRANSFERASE; ALPHA FETOPROTEIN; ASPARTATE AMINOTRANSFERASE; BILIRUBIN; GAMMA GLUTAMYLTRANSFERASE; HEMOGLOBIN; URSODEOXYCHOLIC ACID;

ADOLESCENT; ALANINE AMINOTRANSFERASE BLOOD LEVEL; ALPHA 1 ANTITRYPSIN DEFICIENCY; ARTICLE; ASPARTATE AMINOTRANSFERASE BLOOD LEVEL; BILIRUBIN BLOOD LEVEL; CHILD; CLINICAL ARTICLE; CLINICAL EXAMINATION; CONTROLLED STUDY; DIAGNOSTIC VALUE; DISEASE ASSOCIATION; DISEASE SEVERITY; DRUG EFFECT; FEMALE; FOLLOW UP; GAMMA GLUTAMYL TRANSFERASE BLOOD LEVEL; HEMOGLOBIN BLOOD LEVEL; HEPATOMEGALY; HUMAN; LEUKOCYTE COUNT; LIVER CIRRHOSIS; LIVER DISEASE; LIVER FUNCTION TEST; LIVER TRANSPLANTATION; MALE; OBSTRUCTIVE JAUNDICE; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; PROTHROMBIN TIME; RELAPSE; SCHOOL CHILD; SPLENOMEGALY; THROMBOCYTE COUNT; TREATMENT DURATION; TREATMENT OUTCOME; BLOOD; ENZYMOLOGY; GENETICS; INFANT; NEWBORN; PHENOTYPE; RECURRENT DISEASE; RETROSPECTIVE STUDY;

ALANINE TRANSAMINASE; ALPHA 1-ANTITRYPSIN DEFICIENCY; ASPARTATE AMINOTRANSFERASES; BILIRUBIN; CHILD; CHILD, PRESCHOOL; FEMALE; FOLLOW-UP STUDIES; GAMMA-GLUTAMYLTRANSFERASE; HUMANS; INFANT; INFANT, NEWBORN; LIVER DISEASES; LIVER FUNCTION TESTS; MALE; PHENOTYPE; RECURRENCE; RETROSPECTIVE STUDIES; URSODEOXYCHOLIC ACID;

EID: 59849113007     PISSN: 02772116     EISSN: None     Source Type: Journal    
DOI: 10.1097/MPG.0b013e31817b6dfb     Document Type: Article

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