Reduced expression of sarcospan in muscles of Fukuyama congenital muscular dystrophy

Histology and Histopathology

Volumn 23, Issue 12, 2008, Pages 1425-1438

  Wakayama, Yoshihiro ^a   Inoue, Masahiko ^a   Kojima, Hiroko ^a   Yamashita, Sumimasa ^b   Shibuya, Seiji ^a   Jimi, Takahiro ^a   Hara, Hajime ^a   Matsuzaki, Yoko ^a   Oniki, Hiroaki ^a   Kanagawa, Motoi ^c   Kobayashi, Kazuhiro ^c   Toda, Tatsushi ^c  

^a SHOWA UNIVERSITY FUJIGAOKA HOSPITAL   (Japan)

^b KANAGAWA CHILDREN'S MEDICAL CENTER   (Japan)

^c OSAKA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

Immunoblot; Immunofluorescence; Muscular dystrophy; Real time RT PCR; Sarcospan

Indexed keywords

ALPHA DYSTROGLYCAN; ALPHA SARCOGLYCAN; BETA DYSTROGLYCAN; BETA SARCOGLYCAN; DELTA SARCOGLYCAN; DYSTROPHIN ASSOCIATED PROTEIN; GAMMA SARCOGLYCAN; GLYCERALDEHYDE 3 PHOSPHATE DEHYDROGENASE; MESSENGER RNA; SARCOSPAN; UNCLASSIFIED DRUG; CARRIER PROTEIN; DYSTROGLYCAN; MEMBRANE PROTEIN; SARCOGLYCAN; SSPN PROTEIN, HUMAN; TUMOR PROTEIN;

ADULT; ARTICLE; BASEMENT MEMBRANE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; DUCHENNE MUSCULAR DYSTROPHY; FEMALE; FUKUYAMA CONGENITAL MUSCULAR DYSTROPHY; GOLGI COMPLEX; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; IMMUNOREACTIVITY; INFANT; MALE; MUSCLE CELL; NUCLEOTIDE SEQUENCE; PROTEIN EXPRESSION; PROTEIN GLYCOSYLATION; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; BIOSYNTHESIS; GENE DOSAGE; GENE EXPRESSION; GENE EXPRESSION PROFILING; GENETICS; METABOLISM; MUSCULAR DYSTROPHY; PATHOLOGY; SKELETAL MUSCLE;

CARRIER PROTEINS; DYSTROGLYCANS; FEMALE; GENE DOSAGE; GENE EXPRESSION; GENE EXPRESSION PROFILING; HUMANS; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; INFANT; MALE; MEMBRANE PROTEINS; MUSCLE, SKELETAL; MUSCULAR DYSTROPHIES; NEOPLASM PROTEINS; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RNA, MESSENGER; SARCOGLYCANS;

EID: 58149289767     PISSN: 02133911     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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