Wilson disease as a cause of liver injury in cystic fibrosis

Journal of Cystic Fibrosis

Volumn 8, Issue 1, 2009, Pages 63-65

  Kotalová, Radana ^a   Jirsa, Milan ^b   Vávrová, Věra ^c   Vrábelová Pouchlá, Slávka ^c   Macek Jr , Milan ^a  

^a UNIVERSITY HOSPITAL MOTOL   (Czech Republic)

^b INSTITUTE FOR CLINICAL AND EXPERIMENTAL MEDICINE   (Czech Republic)

^c UNIVERSITY HOSPITAL BRNO   (Czech Republic)

Author keywords

Cholestasis; Cystic fibrosis; Jaundice; Liver disease; Wilson disease

Indexed keywords

PENICILLAMINE; PYRIDOXINE; URSODEOXYCHOLIC ACID;

ALPHA ANTITRYPSIN DEFICIENCY; ARTICLE; CASE REPORT; CAUCASIAN; CYSTIC FIBROSIS; GENETIC DISORDER; GILBERT DISEASE; HOMOZYGOSITY; HUMAN; HUMAN TISSUE; HYPERBILIRUBINEMIA; ILEOSTOMY; LIVER BIOPSY; LIVER INJURY; LUNG DISEASE; MALE; MECONIUM ILEUS; METABOLIC DISORDER; MISSENSE MUTATION; PANCREAS DISEASE; SCHOOL CHILD; WILSON DISEASE;

CHELATING AGENTS; CHILD; CHILD, PRESCHOOL; CYSTIC FIBROSIS; DIAGNOSIS, DIFFERENTIAL; GENETIC SCREENING; GENOTYPE; GILBERT DISEASE; HEPATOLENTICULAR DEGENERATION; HUMANS; INFANT, NEWBORN; INFANT, PREMATURE; LIVER; LIVER FUNCTION TESTS; MALE; MUTATION; PENICILLAMINE; PYRIDOXINE; VITAMIN B COMPLEX;

EID: 57649159159     PISSN: 15691993     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jcf.2008.09.003     Document Type: Article

References (8)

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