Re-evaluation of the penicillamine challenge test in the diagnosis of Wilson's disease in children

Journal of Hepatology

Volumn 47, Issue 2, 2007, Pages 270-276

  Müller, Thomas ^a,d   Koppikar, Smita ^e   Taylor, Rachel M ^e   Carragher, Fiona ^b   Schlenck, Barbara ^b   Heinz Erian, Peter ^a   Kronenberg, Florian ^a   Ferenci, Peter ^a   Tanner, Stuart ^c   Siebert, Uwe ^d,f   Staudinger, Roland ^e   Mieli Vergani, Giorgina ^e   Dhawan, Anil ^e  

^a INNSBRUCK MEDICAL UNIVERSITY   (Austria)

^b KING S COLLEGE HOSPITAL   (United Kingdom)

^c MEDICAL UNIVERSITY OF VIENNA   (Austria)

^d UNIVERSITY OF SHEFFIELD   (United Kingdom)

^e UNIVERSITY FOR HEALTH SCIENCES   (Austria)

^f MASSACHUSETTS GENERAL HOSPITAL   (United States)

Author keywords

Copper; Liver; Penicillamine; Wilson's disease

Indexed keywords

CERULOPLASMIN; COPPER; PENICILLAMINE;

ADOLESCENT; ARTICLE; CERULOPLASMIN BLOOD LEVEL; CONTROLLED STUDY; COPPER BLOOD LEVEL; FEMALE; GENETIC ANALYSIS; HUMAN; HUMAN TISSUE; IRON URINE LEVEL; LIVER DISEASE; LIVER HISTOLOGY; MAJOR CLINICAL STUDY; MALE; PRESCHOOL CHILD; PRIORITY JOURNAL; URINALYSIS; URINARY EXCRETION; WILSON DISEASE;

ADOLESCENT; CERULOPLASMIN; CHELATING AGENTS; CHILD; CHILD, PRESCHOOL; CIRCADIAN RHYTHM; COPPER; DIAGNOSTIC TECHNIQUES, DIGESTIVE SYSTEM; DNA MUTATIONAL ANALYSIS; FEMALE; HEPATOLENTICULAR DEGENERATION; HUMANS; LIVER; MALE; PENICILLAMINE; SENSITIVITY AND SPECIFICITY;

EID: 34347393446     PISSN: 01688278     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jhep.2007.03.011     Document Type: Article

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