Structure-function study of the glucose-6-phosphate transporter, an eukaryotic antiporter deficient in glycogen storage disease type Ib

Molecular Genetics and Metabolism

Volumn 96, Issue 1, 2009, Pages 32-37

  Pan, Chi Jiunn ^a   Chen, Shih Yin ^a   Lee, Soojung ^a   Chou, Janice Y ^a  

^a EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

Author keywords

Antiporter; Endoplasmic reticulum; G6P transport; Glycogen storage disease type I; Glycosylation scanning; Phosphate transport

Indexed keywords

AMINO ACID; ANTIPORTER; GLUCOSE 6 PHOSPHATE TRANSPORTER; HEXOSE PHOSPHATE; HEXOSE PHOSPHATE TRANSPORTER UHPT; PHOSPHATE TRANSPORTER; PROTEINASE; UNCLASSIFIED DRUG;

ARTICLE; ENDOPLASMIC RETICULUM; ENZYME ACTIVITY; ENZYME ASSAY; ENZYME BINDING; ENZYME LOCALIZATION; ENZYME SUBSTRATE; GLYCOGEN STORAGE DISEASE TYPE 1; HETEROLOGOUS EXPRESSION; IN VITRO STUDY; MOLECULAR MODEL; PRIORITY JOURNAL; PROTEIN DOMAIN; PROTEIN FUNCTION; PROTEIN GLYCOSYLATION; SEQUENCE HOMOLOGY; SITE DIRECTED MUTAGENESIS; STRUCTURE ACTIVITY RELATION; X RAY CRYSTALLOGRAPHY;

AMINO ACID SEQUENCE; ANIMALS; BIOLOGICAL TRANSPORT; CERCOPITHECUS AETHIOPS; COS CELLS; GLUCOSE-6-PHOSPHATE; GLYCOGEN STORAGE DISEASE TYPE I; HUMANS; MOLECULAR SEQUENCE DATA; MONOSACCHARIDE TRANSPORT PROTEINS; MUTATION; PROTEIN STRUCTURE, SECONDARY; PROTEIN STRUCTURE, TERTIARY; STRUCTURE-ACTIVITY RELATIONSHIP;

BACTERIA (MICROORGANISMS); EUKARYOTA;

EID: 57649103649     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2008.10.005     Document Type: Article

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