Hereditary haemorrhagic telangiectasia

Haemophilia

Volumn 14, Issue 6, 2008, Pages 1269-1280

  Sharathkumar, A A ^a   Shapiro, A ^a  

^a INDIANA HEMOPHILIA AND THROMBOSIS CENTER   (United States)

Author keywords

Anaemia; Bleeding; Osler Weber Rendu syndrome; Telangiectasia; Transforming growth factor ; Vascular malformations

Indexed keywords

ACTIVIN LIKE RECEPTOR KINASE 1; ALPHA INTERFERON; ANTIBIOTIC AGENT; ANTIFIBRINOLYTIC AGENT; BEVACIZUMAB; CYTOKINE RECEPTOR; ENDOGLIN; ESTROGEN; IRON; PROGESTERONE; TRANEXAMIC ACID; UNCLASSIFIED DRUG; VASCULOTROPIN;

ANEMIA; ARTERIOVENOUS MALFORMATION; ARTIFICIAL EMBOLISM; BLOOD TRANSFUSION; BODY DISTRIBUTION; BRAIN ABSCESS; BRAIN ARTERIOVENOUS MALFORMATION; CLINICAL EXAMINATION; CLINICAL FEATURE; DIAGNOSTIC VALUE; DRUG MEGADOSE; EPISTAXIS; FAMILIAL DISEASE; GASTROINTESTINAL SYMPTOM; GENE MUTATION; GENETIC ASSOCIATION; GENETIC SCREENING; HEPATIC ARTERIOVENOUS MALFORMATION; HUMAN; IMAGE ANALYSIS; LASER COAGULATION; LIVER TRANSPLANTATION; LOW LEVEL LASER THERAPY; LUNG TRANSPLANTATION; MOLECULAR DYNAMICS; MOLECULAR MECHANICS; PATHOGENESIS; PRIORITY JOURNAL; PROGNOSIS; PULMONARY ARTERIOVENOUS FISTULA; RENDU OSLER WEBER DISEASE; REVIEW; SKIN MANIFESTATION; TELANGIECTASIA; VASCULAR SURGERY;

ADULT; AGED; CHILD; DIAGNOSIS, DIFFERENTIAL; EMBOLIZATION, THERAPEUTIC; EPISTAXIS; FEMALE; GENETIC SCREENING; HEMORRHAGE; HUMANS; INFANT, NEWBORN; MAGNETIC RESONANCE IMAGING; MALE; MIDDLE AGED; MOUTH MUCOSA; MUTATION; NASAL MUCOSA; PHENOTYPE; PREGNANCY; TELANGIECTASIA, HEREDITARY HEMORRHAGIC; TELANGIECTASIS; TOMOGRAPHY, X-RAY COMPUTED;

EID: 55949124815     PISSN: 13518216     EISSN: 13652516     Source Type: Journal    
DOI: 10.1111/j.1365-2516.2008.01774.x     Document Type: Review

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