메뉴 건너뛰기




Volumn 295, Issue 2, 2008, Pages

From the farm to the lab: The pig as a new model of cystic fibrosis lung disease

Author keywords

[No Author keywords available]

Indexed keywords

CHLORIDE CHANNEL; CYCLIC AMP; TRANSMEMBRANE CONDUCTANCE REGULATOR;

EID: 52149092776     PISSN: 10400605     EISSN: 15221504     Source Type: Journal    
DOI: 10.1152/ajplung.90311.2008     Document Type: Note
Times cited : (4)

References (21)
  • 1
    • 34347333381 scopus 로고    scopus 로고
    • Molecular targeting of CFTR as a therapeutic approach to cystic fibrosis
    • Amaral MD, Kunzelmann K. Molecular targeting of CFTR as a therapeutic approach to cystic fibrosis. Trends Pharmacol Sci 28: 334-341, 2007.
    • (2007) Trends Pharmacol Sci , vol.28 , pp. 334-341
    • Amaral, M.D.1    Kunzelmann, K.2
  • 5
    • 34249662628 scopus 로고    scopus 로고
    • Cystic fibrosis: A disease of vulnerability to airway surface dehydration
    • Boucher RC. Cystic fibrosis: a disease of vulnerability to airway surface dehydration. Trends Mol Med 13: 231-240, 2007.
    • (2007) Trends Mol Med , vol.13 , pp. 231-240
    • Boucher, R.C.1
  • 7
    • 0033696130 scopus 로고    scopus 로고
    • Evidence against the acidification hypothesis in cystic fibrosis
    • Gibson GA, Hill WG, Weisz OA. Evidence against the acidification hypothesis in cystic fibrosis. Am J Physiol Cell Physiol 279: C1088-C1099, 2000.
    • (2000) Am J Physiol Cell Physiol , vol.279
    • Gibson, G.A.1    Hill, W.G.2    Weisz, O.A.3
  • 9
    • 35748973573 scopus 로고    scopus 로고
    • Cystic fibrosis transmembrane conductance regulator independent phagosomal acidification in macrophages
    • Haggie PM, Verkman AS. Cystic fibrosis transmembrane conductance regulator independent phagosomal acidification in macrophages. J Biol Chem 282: 31422-31428, 2007.
    • (2007) J Biol Chem , vol.282 , pp. 31422-31428
    • Haggie, P.M.1    Verkman, A.S.2
  • 10
    • 0035132659 scopus 로고    scopus 로고
    • Noninvasive in vivo fluorescence measurement of airway-surface liquid depth, salt concentration, and pH
    • Jayaraman S, Song Y, Vetrivel L, Shankar L, Verkman AS. Noninvasive in vivo fluorescence measurement of airway-surface liquid depth, salt concentration, and pH. J Clin Invest 107: 317-324 2001.
    • (2001) J Clin Invest , vol.107 , pp. 317-324
    • Jayaraman, S.1    Song, Y.2    Vetrivel, L.3    Shankar, L.4    Verkman, A.S.5
  • 11
    • 0032433707 scopus 로고    scopus 로고
    • Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
    • Matsui H, Grubb BR, Tarran R, Randell SH, Gatzy JT, Davis CW, Boucher RC. Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease. Cell 95: 1005-1115, 1998.
    • (1998) Cell , vol.95 , pp. 1005-1115
    • Matsui, H.1    Grubb, B.R.2    Tarran, R.3    Randell, S.H.4    Gatzy, J.T.5    Davis, C.W.6    Boucher, R.C.7
  • 13
    • 24644464284 scopus 로고    scopus 로고
    • Small-molecule correctors of defective ΔF508-CFTR cellular processing identified by high-throughput screening
    • Pedemonte N, Lukacs GL, Du K, Caci E, Zegarra-Moran O, Galietta LJ, Verkman AS. Small-molecule correctors of defective ΔF508-CFTR cellular processing identified by high-throughput screening. J Clin Invest 115: 2564-2571, 2005.
    • (2005) J Clin Invest , vol.115 , pp. 2564-2571
    • Pedemonte, N.1    Lukacs, G.L.2    Du, K.3    Caci, E.4    Zegarra-Moran, O.5    Galietta, L.J.6    Verkman, A.S.7
  • 17
    • 0029984180 scopus 로고    scopus 로고
    • Evidence against defective trans-Golgi acidification in cystic fibrosis
    • Seksek O, Biwersi J, Verkman AS. Evidence against defective trans-Golgi acidification in cystic fibrosis. J Biol Chem 271: 15542-15548, 1996.
    • (1996) J Biol Chem , vol.271 , pp. 15542-15548
    • Seksek, O.1    Biwersi, J.2    Verkman, A.S.3
  • 18
    • 0029870085 scopus 로고    scopus 로고
    • Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid
    • Smith JJ, Travis SM, Greenberg EP, Welsh MJ. Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid. Cell 85: 229-236, 1996.
    • (1996) Cell , vol.85 , pp. 229-236
    • Smith, J.J.1    Travis, S.M.2    Greenberg, E.P.3    Welsh, M.J.4
  • 19
    • 3843101723 scopus 로고    scopus 로고
    • A small molecule CFTR inhibitor produces cystic fibrosis-like submucosal gland fluid secretions in normal airways
    • Thiagarajah JR, Song Y, Haggie PM, Verkman AS. A small molecule CFTR inhibitor produces cystic fibrosis-like submucosal gland fluid secretions in normal airways. FASEB J 18: 875-877, 2004.
    • (2004) FASEB J , vol.18 , pp. 875-877
    • Thiagarajah, J.R.1    Song, Y.2    Haggie, P.M.3    Verkman, A.S.4
  • 21
    • 0037213623 scopus 로고    scopus 로고
    • Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease
    • Verkman AS, Song Y, Thiagarajah JR. Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease. Am J Physiol Cell Physiol 284: C2-C15, 2003.
    • (2003) Am J Physiol Cell Physiol , vol.284
    • Verkman, A.S.1    Song, Y.2    Thiagarajah, J.R.3


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.