Amino acid clearance during acute metabolic decompensation in maple syrup urine disease treated with continuous venovenous hemodialysis with filtration

Pediatric Critical Care Medicine

Volumn 5, Issue 3, 2004, Pages 278-281

  Hmiel, Stanley Paul ^a   Martin, Rick A ^a   Landt, Michael ^a   Levy, Fiona H ^a   Grange, Dorothy K ^a  

^a ST LOUIS CHILDREN S HOSPITAL   (United States)

Author keywords

Amino acid clearance; Continuous venovenous hemofiltration dialysis; Maple syrup urine disease

Indexed keywords

AMINO ACID; LEUCINE;

ACUTE DISEASE; ARTICLE; BLOOD; CASE REPORT; CHILD; HEMODIAFILTRATION; HUMAN; MALE; MAPLE SYRUP URINE DISEASE; METABOLISM; TIME;

ACUTE DISEASE; AMINO ACIDS; CHILD; HEMODIAFILTRATION; HUMANS; LEUCINE; MALE; MAPLE SYRUP URINE DISEASE; TIME FACTORS;

EID: 5144226806     PISSN: 15297535     EISSN: 19473893     Source Type: Journal    
DOI: 10.1097/01.PCC.0000113265.92664.91     Document Type: Article

References (11)

1. Schadewaldt P, Wendel U: Metabolism of branched-chain amino acids in maple syrup urine disease. Eur J Pediatr 1997; 156(Suppl 1):S62-S66
2. Morton DH, Strauss KA, Robinson DL, et al: Diagnosis and treatment of maple syrup disease: A study of 36 patients. Pediatrics 2002; 109:999-1008
3. Puliyanda DP, Harmon WE, Peterschmitt MJ, et al: Utility of hemodialysis in maple syrup urine disease. Pediatr Nephrol 2002; 17:239-242
4. Nyhan WL, Rice-Kelts M, Klein J, et al: Treatment of the acute crisis in maple syrup urine disease. Arch Pediatr Adolesc Med 1998; 152: 593-598
5. Jouvet P, Poggi F, Rabier D, et al: Continuous venovenous haemodiafiltration in the acute phase of neonatal maple syrup urine disease. J Inherit Metab Dis 1997; 20: 463-472
6. Jouvet P, Jugie M, Rabier D, et al: Combined nutritional support and continuous extracorporeal removal therapy in the severe acute phase of maple syrup urine disease. Intensive Care Med 2001; 27:1798-1806
7. Bunchman TE, Maxvold NJ, Barnett J, et al: Pediatric hemofiltration: Normocarb dialysate solution with citrate anticoagulation. Pediatr Nephrol 2002; 17:150-154
8. Gouyon JB, Semama D, Prevot A, et al: Removal of branched-chain amino acids and alpha-ketoisocaproate by haemofiltration and haemodiafiltration. J Inherit Metab Dis 1996; 19:610-620
9. Davenport A, Roberts NB: Amino acid losses during continuous high-flux hemofiltration in the critically ill patient. Crit Care Med 1989; 17:1010-1014
10. Davies SP, Reaveley DA, Brown EA, et al: Amino acid clearance and daily losses in patients with acute renal failure treated by continuous arteriovenous hemodialysis. Crit Care Med 1991; 19:1510-1515
11. Maxvold NJ, Smoyer WE, Custer JR, et al: Amino acid loss and nitrogen balance in critically ill children with acute renal failure: A prospective comparison between classic hemofiltration and hemofiltration with dialysis. Crit Care Med 2000; 28:1161-1165