Hypocomplementemic autosomal recessive hemolytic uremic syndrome with decreased factor H

Pediatric Nephrology

Volumn 12, Issue 8, 1998, Pages 619-624

  Ohali, Melly ^a   Shalev, Hanna ^b   Schlesinger, Menachem ^a   Katz, Yitzhak ^c   Kachko, Leonid ^b   Carmi, Rivka ^b   Sofer, Shaul ^b   Landau, Daniel ^b  

^a BARZILAI MEDICAL CENTER   (Israel)

^b BEN GURION UNIVERSITY OF THE NEGEV   (Israel)

^c TEL AVIV UNIVERSITY   (Israel)

Author keywords

Complement components; Familial; Hemolytic uremic syndrome; Thrombotic microangiopathy

Indexed keywords

COMPLEMENT COMPONENT C3; COMPLEMENT FACTOR H;

ARAB; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; CLINICAL ARTICLE; COMPLEMENT ACTIVATION; DIALYSIS; DISEASE COURSE; ENDOTHELIUM CELL; FEMALE; FIBROBLAST; GLOMERULOPATHY; HEMOLYTIC UREMIC SYNDROME; HUMAN; IMMUNOFLUORESCENCE; INBREEDING; INFANT; KIDNEY BIOPSY; MALE; NEWBORN; PLASMA TRANSFUSION; PRIORITY JOURNAL; THROMBOTIC THROMBOCYTOPENIC PURPURA;

ARABS; COMPLEMENT C3; COMPLEMENT FACTOR H; FEMALE; HEMOLYTIC-UREMIC SYNDROME; HUMANS; INFANT, NEWBORN; ISRAEL; KIDNEY; MALE; MICROSCOPY, ELECTRON; PEDIGREE; TREATMENT OUTCOME;

EID: 0031693194     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004670050515     Document Type: Article

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