Surfactant composition and function in patients with ABCA3 mutations

Pediatric Research

Volumn 59, Issue 6, 2006, Pages 801-805

  Garmany, Tami H ^a   Moxley, Michael A ^b   White, Frances V ^c   Dean, Michael ^d   Hull, William M ^e   Whitsett, Jeffrey A ^e   Nogee, Lawrence M ^f   Hamvas, Aaron ^a  

^a ST LOUIS CHILDREN S HOSPITAL   (United States)

^b SAINT LOUIS UNIVERSITY   (United States)

^c WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d NATIONAL CANCER INSTITUTE   (United States)

^e CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^f JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

PHOSPHATIDYLCHOLINE; PROTEIN; PROTEIN ATP BINDING CASSETTE TRANSPORTER A3; UNCLASSIFIED DRUG; ABC TRANSPORTER; ABCA3 PROTEIN, HUMAN; LUNG SURFACTANT; SURFACTANT PROTEIN B;

ARTICLE; CELL INCLUSION; CLINICAL ARTICLE; CONTROLLED STUDY; DISEASE ASSOCIATION; FEMALE; GENE MUTATION; HOMEOSTASIS; HUMAN; HUMAN CELL; HUMAN TISSUE; LIPID COMPOSITION; LUNG LAVAGE; LUNG TRANSPLANTATION; MALE; MOLECULAR RECOGNITION; PRIORITY JOURNAL; PROTEIN FUNCTION; RESPIRATORY DISTRESS; SURFACE TENSION; THIN LAYER CHROMATOGRAPHY; CASE CONTROL STUDY; GENETICS; INFANT; METABOLISM; MUTATION;

ATP-BINDING CASSETTE TRANSPORTERS; BRONCHOALVEOLAR LAVAGE FLUID; CASE-CONTROL STUDIES; CHROMATOGRAPHY, THIN LAYER; HUMANS; INFANT; MUTATION; PULMONARY SURFACTANT-ASSOCIATED PROTEIN B; PULMONARY SURFACTANTS;

EID: 33746482871     PISSN: 00313998     EISSN: None     Source Type: Journal    
DOI: 10.1203/01.pdr.0000219311.14291.df     Document Type: Article

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