Lymphangioleiomyomatosis and tuberous sclerosis complex

Lung

Volumn 186, Issue 4, 2008, Pages 197-207

  Chorianopoulos, Dimitrios ^a,b,c   Stratakos, Grigoris ^a  

^a UNIVERSITY OF ATHENS MEDICAL SCHOOL   (Greece)

^b EVANGELISMOS HOSPITAL   (Greece)

^c NONE   (Greece)

Author keywords

Lymphangioleiomyomatosis; Somatic mutation; TSC 2; Tuberous sclerosis complex

Indexed keywords

BETA 2 ADRENERGIC RECEPTOR STIMULATING AGENT; BISPHOSPHONIC ACID DERIVATIVE; BRONCHODILATING AGENT; CORTICOSTEROID; DOXYCYCLINE; GESTAGEN; GONADORELIN; GOSERELIN; HAMARTIN; INFLUENZA VACCINE; MATRIX METALLOPROTEINASE; MEDROXYPROGESTERONE; NORETHISTERONE ACETATE; PROGESTERONE; RAPAMYCIN; S6 KINASE; TISSUE INHIBITOR OF METALLOPROTEINASE; TUBERIN;

ANGIOMYOLIPOMA; AUTOSOMAL INHERITANCE; CELL PROLIFERATION; CHROMOSOME 16P; CHROMOSOME 9Q; CLINICAL FEATURE; ENZYME ACTIVATION; LUNG TRANSPLANTATION; LYMPHANGIOLEIOMYOMATOSIS; OVARIECTOMY; PATHOGENESIS; PNEUMOTHORAX; PREGNANCY; PRIORITY JOURNAL; PROGNOSIS; RESPIRATORY FAILURE; REVIEW; SOMATIC MUTATION; TSC1 GENE; TSC2 GENE; TUBEROUS SCLEROSIS; TUMOR SUPPRESSOR GENE;

DISEASE PROGRESSION; GENETIC PREDISPOSITION TO DISEASE; HUMANS; LUNG; LYMPHANGIOLEIOMYOMATOSIS; MATRIX METALLOPROTEINASES; RISK FACTORS; TISSUE INHIBITOR OF METALLOPROTEINASES; TREATMENT OUTCOME; TUBEROUS SCLEROSIS;

EID: 47549087154     PISSN: 03412040     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00408-008-9087-5     Document Type: Review

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