Nephroangiosclerosis in Cerebral Autosomal Dominant Arteriopathy With Subcortical Infarcts and Leukoencephalopathy: Is NOTCH3 Mutation the Common Culprit?

American Journal of Kidney Diseases

Volumn 52, Issue 2, 2008, Pages 340-345

  Guerrot, Dominique ^a,b   François, Arnaud ^a   Boffa, Jean Jacques ^b,c,d   Boulos, Nada ^b,c   Hanoy, Melanie ^a   Legallicier, Bruno ^a   Triquenot Bagan, Aude ^a   Guyant Marechal, Lucie ^a   Laquerriere, Annie ^a   Freguin Bouilland, Caroline ^a   Ronco, Pierre ^b,c,d   Godin, Michel ^a  

^a ROUEN UNIVERSITY HOSPITAL   (France)

^b INSERM   (France)

^c SORBONNE UNIVERSITÉ   (France)

^d HÔPITAL TENON   (France)

Author keywords

Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy (CADASIL); kidney disease; nephroangiosclerosis; NOTCH

Indexed keywords

IMMUNOGLOBULIN A; NOTCH3 RECEPTOR;

ADULT; ARTERIOSCLEROSIS; ARTICLE; CADASIL; CARDIOVASCULAR RISK; CASE REPORT; CHRONIC KIDNEY DISEASE; DEMENTIA; DISEASE SEVERITY; ELECTRON MICROSCOPY; FIBROSING ALVEOLITIS; GENE MUTATION; GLOMERULUS; GLOMERULUS FILTRATION RATE; HEMATURIA; HISTOLOGY; HUMAN; HYPERTENSION; IMMUNOGLOBULIN A NEPHROPATHY; KIDNEY DISEASE; KIDNEY FUNCTION; KIDNEY INJURY; MALE; MENTAL DISEASE; MESANGIUM; PATHOGENESIS; PROTEINURIA; RISK FACTOR; SMOOTH MUSCLE FIBER; STROKE; VASCULAR DISEASE;

ARTERIOLOSCLEROSIS; BIOPSY; CADASIL; CELL PROLIFERATION; DNA; DNA MUTATIONAL ANALYSIS; FOLLOW-UP STUDIES; GLOMERULONEPHRITIS, IGA; HUMANS; IMMUNOHISTOCHEMISTRY; JUXTAGLOMERULAR APPARATUS; MAGNETIC RESONANCE IMAGING; MALE; MESANGIAL CELLS; MICROSCOPY, ELECTRON; MIDDLE AGED; MUSCLE, SMOOTH, VASCULAR; MUTATION, MISSENSE; RECEPTORS, NOTCH; RENAL ARTERY; RENAL CIRCULATION; ULTRASONOGRAPHY, DOPPLER;

EID: 47149098061     PISSN: 02726386     EISSN: None     Source Type: Journal    
DOI: 10.1053/j.ajkd.2008.04.017     Document Type: Article

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