Elevation of lung surfactant phosphatidylcholine in mouse models of Sandhoff and of Niemann-Pick A disease

Journal of Inherited Metabolic Disease

Volumn 27, Issue 5, 2004, Pages 641-648

  Buccoliero, R ^a   Ginzburg, L ^a   Futerman, A H ^a  

^a WEIZMANN INSTITUTE OF SCIENCE   (Israel)

Author keywords

[No Author keywords available]

Indexed keywords

LIPID; LUNG SURFACTANT; PHOSPHATE; PHOSPHATIDYLCHOLINE; PHOSPHOLIPID; SPHINGOLIPID; SPHINGOMYELIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DEATH; DISEASE PREDISPOSITION; EXTRACTION; LUNG LAVAGE; LUNG PARENCHYMA; MOUSE; MOUSE STRAIN; NIEMANN PICK DISEASE; NONHUMAN; PATHOLOGY; QUANTITATIVE ANALYSIS; RESPIRATORY TRACT INFECTION; SANDHOFF DISEASE;

ANIMALS; DISEASE MODELS, ANIMAL; HETEROZYGOTE; HUMANS; LIPID METABOLISM; LIPIDS; LUNG; MICE; NIEMANN-PICK DISEASES; PHOSPHATES; PHOSPHATIDYLCHOLINES; PHOSPHOLIPIDS; PULMONARY SURFACTANTS; SANDHOFF DISEASE; TIME FACTORS;

EID: 4644371271     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/B:BOLI.0000042958.22066.6c     Document Type: Article

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