Natural history of hepatic glycogen storage diseases;Histoire naturelle des glycogénoses avec atteinte hépatique

Presse Medicale

Volumn 37, Issue 7-8, 2008, Pages 1172-1177

  Labrune, Philippe ^a,b   Eberschweiler, Pascale Trioche ^a,b   Boudjemline, Alix Mollet ^a,b   Hubert Buron, Aurélie ^a,b   Petit, François ^a,b   Gajdos, Vincent ^a,b  

^a ASSISTANCE PUBLIQUE HÔPITAUX DE PARIS   (France)

^b UNIVERSITÉ PARIS SACLAY   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA FETOPROTEIN; AMYLO 1,6 GLUCOSIDASE; CORTICOSTEROID; DESMOPRESSIN; DIPEPTIDYL CARBOXYPEPTIDASE INHIBITOR; GLUCOSE; GLUCOSE 6 PHOSPHATASE; GLYCOGEN SYNTHASE;

ANAMNESIS; BLEEDING; CHILDBIRTH; CHOLELITHIASIS; COGNITIVE DEVELOPMENT; CONTRACEPTION; CORTICOSTEROID THERAPY; DISEASE ACTIVITY; DISEASE COURSE; DRUG CONTRAINDICATION; EPISTAXIS; GENITAL TRACT INFECTION; GINGIVITIS; GLUCOSE BLOOD LEVEL; GLYCOGEN STORAGE DISEASE; GLYCOGEN STORAGE DISEASE TYPE 1; GLYCOGEN STORAGE DISEASE TYPE 3; GLYCOGEN STORAGE DISEASE TYPE 4; GLYCOGEN STORAGE DISEASE TYPE 6; GLYCOGENOLYSIS; HEART FUNCTION; HEPATOMEGALY; HUMAN; HYPERCHOLESTEROLEMIA; HYPERLIPIDEMIA; HYPERTRIGLYCERIDEMIA; HYPERURICEMIA; HYPOGLYCEMIC COMA; INFECTION RISK; INTELLIGENCE QUOTIENT; KIDNEY CALCIFICATION; KIDNEY FUNCTION; KIDNEY TRANSPLANTATION; LIVER ADENOMA; LIVER CARCINOMA; LIVER CIRRHOSIS; LIVER FIBROSIS; LIVER TRANSPLANTATION; LONG TERM CARE; MICROALBUMINURIA; MORTALITY; MOUTH ULCER; MUCOSA; MUSCLE FATIGUE; MUSCLE WEAKNESS; MYOPATHY; NEPHROLITHIASIS; NERVOUS SYSTEM DEVELOPMENT; NEUTROPENIA; PANCREATITIS; PATIENT MONITORING; PERIODONTITIS; PREGNANCY; PROGNOSIS; PROTEIN BLOOD LEVEL; PROTEINURIA; PUBERTY; PULMONARY HYPERTENSION; SHORT SURVEY; THROMBOCYTE ANOMALY; TREATMENT PLANNING;

GLYCOGEN STORAGE DISEASE TYPE I; GLYCOGEN STORAGE DISEASE TYPE III; GLYCOGEN STORAGE DISEASE TYPE IV; GROWTH; HUMANS; LIVER DISEASES; MUSCLE, SKELETAL; TREATMENT OUTCOME;

EID: 45449101159     PISSN: 07554982     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.lpm.2007.09.023     Document Type: Short Survey

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