Glycogen storage disease type I: Pathophysiology of liver adenomas

European Journal of Pediatrics, Supplement

Volumn 161, Issue 1, 2002, Pages

  Lee, Philip J ^a  

^a NATIONAL HOSPITAL FOR NEUROLOGY AND NEUROSURGERY   (United Kingdom)

Author keywords

Glycogenosis; Hepatocellular carcinoma; Hepatoma; Liver adenoma; Liver transplantation

Indexed keywords

CONFERENCE PAPER; DIET THERAPY; GLYCOGEN STORAGE DISEASE TYPE 1; HUMAN; INCIDENCE; LIVER ADENOMA; LIVER RESECTION; LIVER TRANSPLANTATION; MALIGNANT TRANSFORMATION; METABOLIC REGULATION; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL;

EID: 0036387477     PISSN: 09439676     EISSN: None     Source Type: Journal    
DOI: 10.1007/bf02679993     Document Type: Conference Paper

References (14)

1. Bianchi L (1993) Glycogen storage disease I and hepatocellular tumours. Eur J Pediatr 152[Suppl 1]: S63-S70
2. Conti JA, Kemeny N (1992) Type Ia glycogenosis associated with hepatocellular carcinoma. Cancer 69: 1320-1322
3. De Parscau L, Guibaud P, Labrune P, Odievre M (1988) Évolution à long terme des glycogenoses hépatiques. Arch Franç Pediatr 45: 641-645
4. Labrune P, Trioche P, Duvaltier I, Chevalier P, Odievre M (1997) Hepatocellular adenomas in glycogen storage disease type I and III: a series of 43 patients and review of the literature. J Pediatr Gastroenterol Nutr 24: 276-279
5. Lee P, Mather S, Owen C, Leonard J, Dicks-Mireaux C (1994) A variety of hepatic ultrasound findings exist in the hepatic glycogen storage diseases. Brit J Radiol 67: 1062-1066
6. Lee PJ, Leonard JV, Dicks-Mireaux C (1995) Focal fatty liver change in glycogenosis type Ia. Eur J Pediatr 154: 332
7. Limmer J, Fleig WE, Leupold D, Bittner R, Ditschneit H, Berger H-G (1988) Hepatocellular carcinoma in type I glycogen storage disease. Hepatology 8: 531-537
8. Mason HH, Andersen DH (1955) Glycogen disease of the liver (von Gierke's disease) with hepatomata: case report with metabolic studies. Pediatrics 16: 785-799
9. Matern D, Starzl TE, Arnaout W, Barnard J, Bynon J, Dhawan A, Emond J, Haagsma EB, Hug G, Lachaux A, Smit GPA, Chen Y-T (1999) Liver transplantation of glycogen storage disease types I, III, and IV. Eur J Pediatr 158[Suppl 2]: S43-S48
10. Ockner RK, Kaikaus RM, Bass NM (1993) Fatty-acid metabolism and the pathogenesis of hepatocellular carcinoma: review and hypothesis. Hepatology 18: 669-676
11. Parker P, Burr I, Slonim A, Ghishan FK, Greene H (1981) Regression of hepatic adenomas in type Ia glycogen storage disease with dietary therapy. Gastroenterology 81: 534-536
12. Smit GPA, Fernandes J, Leonard JV, Matthews EE, Moses SW, Odievre M, Ullrich K (1990) The long-term outcome of patients with glycogen storage diseases. J Inherit Metab Dis 13: 411-418
13. Talente GM, Coleman RA, Alter C, Baker L, Brown BI, Cannon RA, Chen Y-T, Crigler JF, Ferreira P, Haworth JC, Herman GE, Issenman RM, Keating JP, Linde R, Roe TF, Senior B, Wolfsdorf JI (1994) Glycogen storage disease in adults. Ann Intern Med 120: 218-226
14. Wolfsdorf JI, Gutierrez ME, Crigler JF (1994) Determinants of focal hepatic lesions in type I glycogenosis (GSD-I). Pediatr Res 35: 209A