Transport kinetics of FMRP containing the I304N mutation of severe fragile X syndrome in neurites of living rat PC12 cells

Experimental Neurology

Volumn 189, Issue 2, 2004, Pages 343-353

  Schrier, Mariëtte ^a   Severijnen, Lies Anne ^a   Reis, Surya ^a   Rife, Maria ^a   Van't Padje, Sandra ^a   Van Cappellen, Gert ^a   Oostra, Ben A ^a   Willemsen, Rob ^a  

^a ERASMUS MEDICAL CENTER   (Netherlands)

Author keywords

Dendritic mRNA transport; Fragile X syndrome; Microtubules; RNP particle; Time lapse microscopy

Indexed keywords

EPIDERMAL GROWTH FACTOR; FRAGILE X MENTAL RETARDATION PROTEIN; GROWTH FACTOR; HYBRID PROTEIN; RIBOSOME PROTEIN;

ANIMAL CELL; ARTICLE; BLEACHING; CELL GRANULE; CELL STRAIN; COMPLEX FORMATION; CONTROLLED STUDY; DISEASE SEVERITY; FRAGILE X MENTAL RETARDATION GENE; FRAGILE X SYNDROME; GENE; GENE INDUCTION; GENE LOCATION; GENE MUTATION; GENETIC TRANSFECTION; IMMUNOPRECIPITATION; MICROSCOPY; MICROTUBULE; MISSENSE MUTATION; MOLECULAR INTERACTION; MOLECULAR MECHANICS; NEURITE; NONHUMAN; PRIORITY JOURNAL; PROTEIN TRANSPORT; RAT;

AMINO ACID SUBSTITUTION; ANIMALS; AXONAL TRANSPORT; CYTOPLASMIC GRANULES; FRAGILE X MENTAL RETARDATION PROTEIN; FRAGILE X SYNDROME; GREEN FLUORESCENT PROTEINS; KINETICS; LUMINESCENT PROTEINS; MACROMOLECULAR SUBSTANCES; MICROTUBULES; MUTATION; MYELIN P0 PROTEIN; NERVE TISSUE PROTEINS; NEURITES; PC12 CELLS; PROTEIN TRANSPORT; RATS; RECOMBINANT FUSION PROTEINS; RNA-BINDING PROTEINS;

EID: 4544384380     PISSN: 00144886     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.expneurol.2004.05.039     Document Type: Article

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