Organic Acidemias: A Methylmalonic and Propionic Focus

Journal of Pediatric Nursing

Volumn 23, Issue 3, 2008, Pages 225-233

  Van Gosen, Lori ^a  

^a JOHNS HOPKINS UNIVERSITY   (United States)

Author keywords

Genetics; Inborn errors of metabolism; Methylmalonic acidemia; Pediatrics; Propionic acidemia

Indexed keywords

METHYLMALONIC ACID; PROPIONIC ACID; PROPIONIC ACID DERIVATIVE;

ACIDOSIS; AFTERCARE; ARTICLE; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; EARLY DIAGNOSIS; FLUID THERAPY; GENETIC SCREENING; GENETICS; HEMOFILTRATION; HUMAN; INCIDENCE; LIVER TRANSPLANTATION; METABOLISM; NEWBORN; NEWBORN INTENSIVE CARE; NEWBORN NURSING; NEWBORN SCREENING; NURSE ATTITUDE; NURSING ASSESSMENT; PRENATAL DIAGNOSIS; PROTEIN RESTRICTION; RECESSIVE GENE; SURVIVAL RATE;

ACIDOSIS; AFTERCARE; AMINO ACID METABOLISM, INBORN ERRORS; DIET, PROTEIN-RESTRICTED; EARLY DIAGNOSIS; FLUID THERAPY; GENES, RECESSIVE; GENETIC SCREENING; HEMOFILTRATION; HUMANS; INCIDENCE; INFANT, NEWBORN; INTENSIVE CARE, NEONATAL; LIVER TRANSPLANTATION; METHYLMALONIC ACID; NEONATAL NURSING; NEONATAL SCREENING; NURSE'S ROLE; NURSING ASSESSMENT; PRENATAL DIAGNOSIS; PROPIONIC ACIDS; SURVIVAL RATE;

EID: 43649087986     PISSN: 08825963     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.pedn.2008.02.004     Document Type: Article

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