Pediatric cardiomyopathies related to fatty acid metabolism

Progress in Pediatric Cardiology

Volumn 25, Issue 1, 2008, Pages 69-78

  Hill, Kevin D ^a   Hamid, Rizwan ^a   Exil, Vernat J ^a  

^a VANDERBILT UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Arrythmia; Cardimyopathy; Fatty acid oxidation; Metabolism

Indexed keywords

3 HYDROXYACYL COENZYME A DEHYDROGENASE; ACYL COENZYME A DEHYDROGENASE; ACYLCARNITINE CARNITINE TRANSLOCASE; BETA ADRENERGIC RECEPTOR BLOCKING AGENT; CARNITINE; CARNITINE PALMITOYL TRANSFERASE TYPE 2; DIGOXIN; DIURETIC AGENT; DOBUTAMINE; DOPAMINE; ELECTRON TRANSFERRING FLAVOPROTEIN; ENALAPRIL; FATTY ACID; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE; MEDIUM CHAIN TRIACYLGLYCEROL; MILRINONE; PROTEIN; RIBOFLAVIN; UNCLASSIFIED DRUG;

ARTICLE; ATRIOVENTRICULAR BLOCK; ATTENTION; CARDIOMYOPATHY; CARDIOVASCULAR SYMPTOM; CARNITINE ACYLCARNITINE TRANSLOCASE DEFICIENCY; CARNITINE DEFICIENCY; CARNITINE PALMITOYL TRANSFERASE TYPE II DEFICIENCY; CLINICAL FEATURE; CONGESTIVE CARDIOMYOPATHY; DIAGNOSTIC PROCEDURE; ELECTRON TRANSFER FLAVOPROTEIN DEFICIENCY; ENZYME DEFICIENCY; FATTY ACID METABOLISM; FATTY ACID OXIDATION; HEART ARRHYTHMIA; HEART LEFT BUNDLE BRANCH BLOCK; HEART MUSCLE CONDUCTION DISTURBANCE; HEART VENTRICLE TACHYCARDIA; HUMAN; HYPERTROPHIC CARDIOMYOPATHY; INTERVENTION STUDY; LONG CHAIN 3 HYDROXYACYL COENZYME A DEHYDROGENASE DEFICIENCY; LOW FAT DIET; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE DEFICIENCY; NEWBORN SCREENING; OUTCOME ASSESSMENT; PATIENT ASSESSMENT; PEDIATRICS; PERICARDIAL EFFUSION; PHYSICIAN; PRIORITY JOURNAL; PROTEIN DEFICIENCY; SINUS NODE DYSFUNCTION; SUPRAVENTRICULAR TACHYCARDIA;

EID: 40949095250     PISSN: 10589813     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ppedcard.2007.11.007     Document Type: Article

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