Hypothesis: Proposals for the management of a neonate at risk of hyperammonaemia due to a urea cycle disorder

European Journal of Pediatrics

Volumn 167, Issue 3, 2008, Pages 305-309

  Leonard, James Vivian ^a   Ward Platt, Martin Peter ^b   Morris, Andrew Alan Myles ^c  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

^b ROYAL VICTORIA INFIRMARY   (United Kingdom)

^c ROYAL MANCHESTER CHILDREN S HOSPITAL   (United Kingdom)

Author keywords

Catabolism; Hyperammonaemia; Octreotide; Phenobarbital; Sodium benzoate

Indexed keywords

ACETIC ACID DERIVATIVE; ARGININE; BENZOIC ACID; BUTYRIC ACID DERIVATIVE; GLUCOSE; INSULIN; N ACETYLGLUTAMIC ACID; N CARBAMYLGLUTAMATE; NITROGEN; OCTREOTIDE; PHENYLACETATE SODIUM; SODIUM PHENYLBUTYRATE; SOMATOSTATIN; UNCLASSIFIED DRUG;

ACIDURIA; ARGININOSUCCINIC ACIDURIA; ARTICLE; BIRTH; CATABOLISM; CESAREAN SECTION; CITRULLINEMIA; CONTINUOUS INFUSION; DIALYSIS; FEEDING; HUMAN; HYPERAMMONEMIA; INTENSIVE CARE; METABOLIC DISORDER; NEUROPROTECTION; NITROGEN URINE LEVEL; PERSISTENT HYPERINSULINEMIC HYPOGLYCEMIA OF INFANCY; PRIORITY JOURNAL; RISK MANAGEMENT; UREA CYCLE DISORDER;

ADRENERGIC BETA-ANTAGONISTS; CESAREAN SECTION; GLUCOSE; HUMANS; HYPERAMMONEMIA; INFANT, NEWBORN; INSULIN; METABOLISM, INBORN ERRORS; OCTREOTIDE; RISK FACTORS; UREA;

EID: 39049165141     PISSN: 03406199     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00431-007-0486-z     Document Type: Article

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