Liver transplantation for argininosuccinic aciduria: Clinical, biochemical, and metabolic outcome

Liver Transplantation

Volumn 14, Issue 1, 2008, Pages 41-45

  Newnham, Tanya ^a   Hardikar, Winita ^a   Allen, Katrina ^a   Wellard, R Mark ^b   Hamilton, Charles ^c   Angus, Peter ^d   Jones, Robert ^d   Boneh, Avihu ^a,e  

^a UNIVERSITY OF MELBOURNE   (Australia)

^b QUEENSLAND UNIVERSITY OF TECHNOLOGY   (Australia)

^c West Gippsland Paediatric Group   (Australia)

^d AUSTIN HEALTH   (Australia)

^e ROYAL CHILDREN'S HOSPITAL   (Australia)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; AMMONIA; ARGININE; ARGININOSUCCINIC ACID; BENZOIC ACID; CARBAMAZEPINE; CITRULLINE; GLUCOSE; INSULIN;

ACIDURIA; ADULT; AMINO ACID BLOOD LEVEL; AMMONIA BLOOD LEVEL; ARGININOSUCCINIC ACIDURIA; ARTICLE; ARTIFICIAL VENTILATION; BIOCHEMISTRY; BRAIN DISEASE; BRAIN METABOLISM; CASE REPORT; CLINICAL FEATURE; COMA; DRUG DOSE INCREASE; DRUG DOSE REGIMEN; DRUG WITHDRAWAL; EXCHANGE BLOOD TRANSFUSION; HEPATOMEGALY; HUMAN; INFANT; LETHARGY; LIVER TRANSPLANTATION; MALE; METABOLIC PARAMETERS; NEUROLOGIC DISEASE; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; PERITONEAL DIALYSIS; PRIORITY JOURNAL; QUALITY OF LIFE; TREATMENT OUTCOME; VOMITING; WELLBEING;

AMINO ACID METABOLISM, INBORN ERRORS; ARGININE; ARGININOSUCCINIC ACID; BASAL GANGLIA; BRAIN CHEMISTRY; DOSE-RESPONSE RELATIONSHIP, DRUG; FOLLOW-UP STUDIES; HEPATIC ENCEPHALOPATHY; HUMANS; INFANT, NEWBORN; MAGNETIC RESONANCE SPECTROSCOPY; MALE; OCCIPITAL LOBE; TIME FACTORS;

EID: 38649098501     PISSN: 15276465     EISSN: 15276473     Source Type: Journal    
DOI: 10.1002/lt.21297     Document Type: Article

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