Liver transplantation in urea cycle disorders

European Journal of Pediatrics, Supplement

Volumn 158, Issue 2, 1999, Pages

  Saudubray, J M ^a   Touati, G ^a   Delonlay, P ^a   Jouvet, P ^a   Narcy, C ^a   Laurent, J ^a   Rabier, D ^a   Kamoun, P ^a   Jan, D ^a   Revillon, Y ^a  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

Inborn errors of metabolism; Liver transplantation; Urea cycle disorders

Indexed keywords

ORNITHINE CARBAMOYLTRANSFERASE;

AMINOACIDURIA; ARTICLE; CHILD; DIET THERAPY; ENZYME DEFICIENCY; FEMALE; HETEROZYGOTE; HUMAN; HYPERAMMONEMIA; INBORN ERROR OF METABOLISM; LIVER TRANSPLANTATION; MAJOR CLINICAL STUDY; MALE; OUTCOMES RESEARCH; PRIORITY JOURNAL; PROTEIN DIET; UREA CYCLE; WELLBEING; X CHROMOSOME INACTIVATION;

AMINO ACID METABOLISM, INBORN ERRORS; CARBAMOYL-PHOSPHATE SYNTHASE I DEFICIENCY DISEASE; CHILD; CHILD, PRESCHOOL; CITRULLINEMIA; FEMALE; HUMANS; INFANT; LIVER TRANSPLANTATION; MALE; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; PROGNOSIS; RETROSPECTIVE STUDIES; UREA;

EID: 0032732091     PISSN: 09439676     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

References (19)

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