Reduced muscle-fiber conduction but normal slowing after cold exposure in paramyotonia congenita

Muscle and Nerve

Volumn 37, Issue 1, 2008, Pages 23-26

  Blijham, Paul J ^a   Drost, Gea ^a   Stegeman, Dick F ^a   Zwarts, Machiel J ^a  

^a RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

Cooling; Electromyography; Muscle fiber conduction velocity; Paramyotonia congenita; Sodium channel

Indexed keywords

VOLTAGE GATED SODIUM CHANNEL;

ADULT; ARTICLE; COLD EXPOSURE; COLD SENSITIVITY; CONTROLLED STUDY; COOLING; ELECTROMYOGRAPHY; FAMILY HISTORY; FEMALE; GENE MUTATION; HISTOGRAM; HUMAN; HUMAN EXPERIMENT; MALE; MUSCLE FIBER MEMBRANE CONDUCTANCE; MUSCLE STIFFNESS; NORMAL HUMAN; PRIORITY JOURNAL; ROOM TEMPERATURE; SARCOLEMMA; THOMSEN DISEASE; VOLUNTEER; WEAKNESS; WILD TYPE;

ACTION POTENTIALS; ADULT; COLD; ELECTROMYOGRAPHY; FEMALE; GENETIC PREDISPOSITION TO DISEASE; HUMANS; MALE; MIDDLE AGED; MUSCLE CONTRACTION; MUSCLE FIBERS; MUSCLE, SKELETAL; MUTATION; MYOTONIC DISORDERS; REACTION TIME; SARCOLEMMA; SODIUM CHANNELS; TIME FACTORS;

EID: 37749018427     PISSN: 0148639X     EISSN: 10974598     Source Type: Journal    
DOI: 10.1002/mus.20885     Document Type: Article

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