메뉴 건너뛰기




Volumn 45, Issue 7, 2007, Pages 437-441

Experimental models of Huntington's disease;Modelos experimentales de la enfermedad de Huntington

Author keywords

3 nitropropionic acid; Cellular models; Excitotoxic models; Huntington's disease; Quinolinic acid; Transgenic mice

Indexed keywords

3 NITROPROPIONIC ACID; PRION PROTEIN;

EID: 37349079897     PISSN: 02100010     EISSN: None     Source Type: Journal    
DOI: 10.33588/rn.4507.2007238     Document Type: Review
Times cited : (10)

References (20)
  • 1
    • 33846225133 scopus 로고    scopus 로고
    • Huntington's disease
    • Walker FO. Huntington's disease. Lancet 2007; 369: 218-28.
    • (2007) Lancet , vol.369 , pp. 218-228
    • Walker, F.O.1
  • 2
    • 0038478782 scopus 로고    scopus 로고
    • Huntington's disease: New hope for therapeutics
    • McMurray CT. Huntington's disease: new hope for therapeutics. Trends Neurosci 2001; 24: 32-8.
    • (2001) Trends Neurosci , vol.24 , pp. 32-38
    • McMurray, C.T.1
  • 3
    • 0035504331 scopus 로고    scopus 로고
    • Expression of the Huntington's disease transgene in neural stem cell cultures from R6/2 transgenic mice
    • Chu-LaGraff Q, Kang XW, Messer A. Expression of the Huntington's disease transgene in neural stem cell cultures from R6/2 transgenic mice. Brain Res Bull 2001; 56: 307-12.
    • (2001) Brain Res Bull , vol.56 , pp. 307-312
    • Chu-LaGraff, Q.1    Kang, X.W.2    Messer, A.3
  • 4
    • 0036533795 scopus 로고    scopus 로고
    • Lessons from animal models of Huntington's disease
    • Rubinsztein DC. Lessons from animal models of Huntington's disease. Trends Genet 2002; 18: 202-9.
    • (2002) Trends Genet , vol.18 , pp. 202-209
    • Rubinsztein, D.C.1
  • 5
    • 26844498655 scopus 로고    scopus 로고
    • The use of the R6 transgenic mouse models of Huntington's disease in attempts to develop novel therapeutic strategies
    • Li JY, Popovic N, Brundin P. The use of the R6 transgenic mouse models of Huntington's disease in attempts to develop novel therapeutic strategies. NeuroRx 2005; 2: 447-64.
    • (2005) NeuroRx , vol.2 , pp. 447-464
    • Li, J.Y.1    Popovic, N.2    Brundin, P.3
  • 7
    • 0034737299 scopus 로고    scopus 로고
    • Reversal of neuropathology and motor dysfunction in a conditional model of Huntington's disease
    • Yamamoto A, Lucas JJ, Hen R. Reversal of neuropathology and motor dysfunction in a conditional model of Huntington's disease. Cell 2000; 101: 57-66.
    • (2000) Cell , vol.101 , pp. 57-66
    • Yamamoto, A.1    Lucas, J.J.2    Hen, R.3
  • 8
    • 30744439549 scopus 로고    scopus 로고
    • Progressive phenotype and nuclear accumulation of an amino-terminal cleavage fragment in a transgenic mouse model with inducible expression of full-length mutant huntingtin
    • Tanaka Y, Igarashi S, Nakamura M, Gafni J, Torcassi C, Schilling G, et al. Progressive phenotype and nuclear accumulation of an amino-terminal cleavage fragment in a transgenic mouse model with inducible expression of full-length mutant huntingtin. Neurobiol Dis 2006; 21: 381-91.
    • (2006) Neurobiol Dis , vol.21 , pp. 381-391
    • Tanaka, Y.1    Igarashi, S.2    Nakamura, M.3    Gafni, J.4    Torcassi, C.5    Schilling, G.6
  • 9
    • 33847317865 scopus 로고    scopus 로고
    • Cellular and subcellular localization of Huntington aggregates in the brain of a rat transgenic for Huntington disease
    • Petrasch-Parwez E, Nguyen HP, Bbecke-Schumacher ML, Habbes HW, Wieczorek S, Riess O, et al. Cellular and subcellular localization of Huntington aggregates in the brain of a rat transgenic for Huntington disease. J Comp Neurol 2007; 501: 716-30.
    • (2007) J Comp Neurol , vol.501 , pp. 716-730
    • Petrasch-Parwez, E.1    Nguyen, H.P.2    Bbecke-Schumacher, M.L.3    Habbes, H.W.4    Wieczorek, S.5    Riess, O.6
  • 10
    • 0032191581 scopus 로고    scopus 로고
    • Comparison of intrastriatal injections of quinolinic acid and 3-nitropropionic acid for use in animal models of Huntington's disease
    • Shear DA, Dong J, Gundy CD, Haik-Creguer KL, Dunbar GL. Comparison of intrastriatal injections of quinolinic acid and 3-nitropropionic acid for use in animal models of Huntington's disease. Prog Neuropsychopharmacol Biol Psychiatry 1998; 22: 1217-40.
    • (1998) Prog Neuropsychopharmacol Biol Psychiatry , vol.22 , pp. 1217-1240
    • Shear, D.A.1    Dong, J.2    Gundy, C.D.3    Haik-Creguer, K.L.4    Dunbar, G.L.5
  • 11
    • 0034210634 scopus 로고    scopus 로고
    • Behavior characterization of a model of Huntington's disease in rats, induced by quinolinic acid
    • Francis L, Cruz R, Antúnez I, Rosillo JC. Behavior characterization of a model of Huntington's disease in rats, induced by quinolinic acid. Rev Neurol 2000; 30: 1016-21.
    • (2000) Rev Neurol , vol.30 , pp. 1016-1021
    • Francis, L.1    Cruz, R.2    Antúnez, I.3    Rosillo, J.C.4
  • 12
    • 0036405496 scopus 로고    scopus 로고
    • Striatal and cortical neurochemical changes induced by chronic metabolic compromise in the 3-nitropropionic model of Huntington's disease
    • Blum D, Galas MC, Gall D, Cuvelier L, Schiffmann SN. Striatal and cortical neurochemical changes induced by chronic metabolic compromise in the 3-nitropropionic model of Huntington's disease. Neurobiol Dis 2002; 10: 410-26.
    • (2002) Neurobiol Dis , vol.10 , pp. 410-426
    • Blum, D.1    Galas, M.C.2    Gall, D.3    Cuvelier, L.4    Schiffmann, S.N.5
  • 13
    • 0032815680 scopus 로고    scopus 로고
    • Replicating Huntington's disease phenotype in experimental animals
    • Brouillet E, Conde F, Beal MF, Hantraye P. Replicating Huntington's disease phenotype in experimental animals. Prog Neurobiol 1999; 59: 427-68.
    • (1999) Prog Neurobiol , vol.59 , pp. 427-468
    • Brouillet, E.1    Conde, F.2    Beal, M.F.3    Hantraye, P.4
  • 14
    • 0030997707 scopus 로고    scopus 로고
    • Quantifiable bradykinesia, gait abnormalities and Huntington's disease-like striatal lesions in rats chronically treated with 3-nitropropionic acid
    • Guyot MC, Hantraye P, Dolan R, Palfi S, Maziere M, Brouillet E. Quantifiable bradykinesia, gait abnormalities and Huntington's disease-like striatal lesions in rats chronically treated with 3-nitropropionic acid. Neuroscience 1997; 79: 45-56.
    • (1997) Neuroscience , vol.79 , pp. 45-56
    • Guyot, M.C.1    Hantraye, P.2    Dolan, R.3    Palfi, S.4    Maziere, M.5    Brouillet, E.6
  • 16
    • 14644430451 scopus 로고    scopus 로고
    • Expanded polyglutamine peptides disrupt EGF receptor signaling and glutamate transporter expression in Drosophila
    • Lievens JC, Rival T, Iche M, Chneiweiss H, Birman S. Expanded polyglutamine peptides disrupt EGF receptor signaling and glutamate transporter expression in Drosophila. Hum Mol Genet 2005; 14: 713-24.
    • (2005) Hum Mol Genet , vol.14 , pp. 713-724
    • Lievens, J.C.1    Rival, T.2    Iche, M.3    Chneiweiss, H.4    Birman, S.5
  • 18
    • 33645081706 scopus 로고    scopus 로고
    • Plastic and behavioural abnormalities in experimental Huntington's disease: A crucial role for cholinergic interneurons
    • Piconi B, Pasión E, Sgobio C, Bonsi P, Barone I, Ghigliori V, et al. Plastic and behavioural abnormalities in experimental Huntington's disease: a crucial role for cholinergic interneurons. Neurobiol Dis 2006; 22: 143-52.
    • (2006) Neurobiol Dis , vol.22 , pp. 143-152
    • Piconi, B.1    Pasión, E.2    Sgobio, C.3    Bonsi, P.4    Barone, I.5    Ghigliori, V.6
  • 19
    • 4444350918 scopus 로고    scopus 로고
    • Brain-derived neurotrophic factor regulates the onset and severity of motor dysfunction associated with enkephalinergic neuronal degeneration in Huntington's disease
    • Canal JM, Pineda JR, Torres-Peraza JF, Bosch M, Martín- Ibáñez R, Muñoz MT, et al. Brain-derived neurotrophic factor regulates the onset and severity of motor dysfunction associated with enkephalinergic neuronal degeneration in Huntington's disease. J Neurosci 2004; 24: 7727-39.
    • (2004) J Neurosci , vol.24 , pp. 7727-7739
    • Canal, J.M.1    Pineda, J.R.2    Torres-Peraza, J.F.3    Bosch, M.4    Martín- Ibáñez, R.5    Muñoz, M.T.6
  • 20
    • 0031680014 scopus 로고    scopus 로고
    • A cellular model that recapitulates major pathogenic steps of Huntington's disease
    • Lunkes A, Mandel JL. A cellular model that recapitulates major pathogenic steps of Huntington's disease. Hum Mol Genet 1998; 7: 1355-61.
    • (1998) Hum Mol Genet , vol.7 , pp. 1355-1361
    • Lunkes, A.1    Mandel, J.L.2


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.