Intermediate levels of neuronal palmitoyl-protein Δ-9 desaturase in heterozygotes for murine Batten disease

Molecular Genetics and Metabolism

Volumn 93, Issue 1, 2008, Pages 89-91

  Narayan, Srinivas B ^a   Tan, Lu ^a   Bennett, Michael J ^a,b  

^a CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

Batten disease; cln3 heterozygotes; Palmitoyl protein desaturase

Indexed keywords

ACYL COENZYME A DESATURASE; CLN3 PROTEIN; PALMITOYL COENZYME A; PROTEIN DERIVATIVE; UNCLASSIFIED DRUG;

ANIMAL TISSUE; ARTICLE; BRAIN; CONTROLLED STUDY; ENZYME ACTIVITY; FOLLOW UP; HETEROZYGOTE; KNOCKOUT MOUSE; MOUSE; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PANCREAS; PRIORITY JOURNAL; PROTEIN FUNCTION; WILD TYPE;

ANIMALS; BRAIN; HETEROZYGOTE; MEMBRANE GLYCOPROTEINS; MICE; MICE, KNOCKOUT; MICE, NEUROLOGIC MUTANTS; MOLECULAR CHAPERONES; NEURONAL CEROID-LIPOFUSCINOSES; NEURONS; PANCREAS; THIOLESTER HYDROLASES;

MURINAE; MUS;

EID: 36849084546     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2007.09.005     Document Type: Article

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