Homophenotypic Aα R16H fibrinogen (Kingsport): Uniquely altered polymerization associated with slower fibrinopeptide A than fibrinopeptide B release

Blood Coagulation and Fibrinolysis

Volumn 18, Issue 8, 2007, Pages 731-737

  Galanakis, Dennis K ^a,f   Neerman Arbez, Marguerite ^b   Scheiner, Tomas ^c   Henschen, Agnes ^d   Hubbs, Doris ^e   Nagaswami, Chandrasekaran ^c   Weisel, John W ^c  

^a STONY BROOK UNIVERSITY   (United States)

^b UNIVERSITY OF GENEVA MEDICAL SCHOOL   (Switzerland)

^c UNIVERSITY OF PENNSYLVANIA   (United States)

^d UNIVERSITY OF CALIFORNIA   (United States)

^e EAST TENNESSEE STATE UNIVERSITY   (United States)

^f STONY BROOK UNIVERSITY MEDICAL CENTER   (United States)

Author keywords

Des BB fibrin; Dysfibrinogenemia A R16H; Fibrin clot stiffness; Fibrinogen

Indexed keywords

FIBRINOGEN; FIBRINOPEPTIDE A; FIBRINOPEPTIDE B; IMMUNOGLOBULIN G; MONOMER; FIBRIN; FIBRINOGEN AALPHA; FIBRINOGEN VARIANT; POLYMER; UNCLASSIFIED DRUG;

ARTICLE; BLOOD CLOTTING; CASE REPORT; CONTROLLED STUDY; DNA SEQUENCE; FETUS; FIBRIN POLYMERIZATION; GELATION; GENE AMPLIFICATION; GENE DELETION; GENOTYPE; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HUMAN; INFANT; IONIC STRENGTH; PHENOTYPE; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; RIGIDITY; SCANNING ELECTRON MICROSCOPY; TURBIDIMETRY; YOUNG MODULUS; ADULT; CHEMISTRY; FEMALE; GENETIC PREDISPOSITION; GENETICS; PHYSIOLOGY; SINGLE NUCLEOTIDE POLYMORPHISM;

ADULT; FEMALE; FIBRIN; FIBRINOGEN; FIBRINOGENS, ABNORMAL; FIBRINOPEPTIDE A; GENETIC PREDISPOSITION TO DISEASE; GENOTYPE; HUMANS; PHENOTYPE; POLYMERS; POLYMORPHISM, SINGLE NUCLEOTIDE;

EID: 35848948603     PISSN: 09575235     EISSN: None     Source Type: Journal    
DOI: 10.1097/MBC.0b013e3282f10157     Document Type: Article

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